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Diagnostic value of chest computed tomography images in adult Poland syndrome: a report of two cases

Poland syndrome is a rare congenital developmental deformity characterized by unilateral agenesis or hypoplasia of thoracic wall soft tissue. We report two adult cases of Poland syndrome detected by computed tomography (CT) images. CT images of the two cases depicted an asymmetric chest wall with th...

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Autores principales: Lei, Shaoyang, Gui, Shaogao, Zhang, Haixu, Wang, Yanxia, Liu, Ronghui, Ye, Yufang, Zhang, Shuqian, Fan, Bing
Formato: Online Artículo Texto
Lenguaje:English
Publicado: SAGE Publications 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8743957/
https://www.ncbi.nlm.nih.gov/pubmed/34994238
http://dx.doi.org/10.1177/03000605211069485
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author Lei, Shaoyang
Gui, Shaogao
Zhang, Haixu
Wang, Yanxia
Liu, Ronghui
Ye, Yufang
Zhang, Shuqian
Fan, Bing
author_facet Lei, Shaoyang
Gui, Shaogao
Zhang, Haixu
Wang, Yanxia
Liu, Ronghui
Ye, Yufang
Zhang, Shuqian
Fan, Bing
author_sort Lei, Shaoyang
collection PubMed
description Poland syndrome is a rare congenital developmental deformity characterized by unilateral agenesis or hypoplasia of thoracic wall soft tissue. We report two adult cases of Poland syndrome detected by computed tomography (CT) images. CT images of the two cases depicted an asymmetric chest wall with the absence of a breast and agenesis of the pectoralis muscles. A physical examination of case 1 showed a thin right chest wall with depression of the right nipple region. Hand deformities were also observed, including brachydactyly and syndactyly. In case 2, hand deformities were not found in a physical examination. Using multi-planar reconstruction, the size, position, origin, and termination of bilateral pectoral muscles could be compared symmetrically. For patients with Poland syndrome, a timely diagnosis and treatment are important. The use of chest CT in clinical practice could play an important role in the early diagnosis and treatment of Poland syndrome.
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spelling pubmed-87439572022-01-11 Diagnostic value of chest computed tomography images in adult Poland syndrome: a report of two cases Lei, Shaoyang Gui, Shaogao Zhang, Haixu Wang, Yanxia Liu, Ronghui Ye, Yufang Zhang, Shuqian Fan, Bing J Int Med Res Case Reports Poland syndrome is a rare congenital developmental deformity characterized by unilateral agenesis or hypoplasia of thoracic wall soft tissue. We report two adult cases of Poland syndrome detected by computed tomography (CT) images. CT images of the two cases depicted an asymmetric chest wall with the absence of a breast and agenesis of the pectoralis muscles. A physical examination of case 1 showed a thin right chest wall with depression of the right nipple region. Hand deformities were also observed, including brachydactyly and syndactyly. In case 2, hand deformities were not found in a physical examination. Using multi-planar reconstruction, the size, position, origin, and termination of bilateral pectoral muscles could be compared symmetrically. For patients with Poland syndrome, a timely diagnosis and treatment are important. The use of chest CT in clinical practice could play an important role in the early diagnosis and treatment of Poland syndrome. SAGE Publications 2022-01-07 /pmc/articles/PMC8743957/ /pubmed/34994238 http://dx.doi.org/10.1177/03000605211069485 Text en © The Author(s) 2022 https://creativecommons.org/licenses/by-nc/4.0/Creative Commons Non Commercial CC BY-NC: This article is distributed under the terms of the Creative Commons Attribution-NonCommercial 4.0 License (https://creativecommons.org/licenses/by-nc/4.0/) which permits non-commercial use, reproduction and distribution of the work without further permission provided the original work is attributed as specified on the SAGE and Open Access pages (https://us.sagepub.com/en-us/nam/open-access-at-sage).
spellingShingle Case Reports
Lei, Shaoyang
Gui, Shaogao
Zhang, Haixu
Wang, Yanxia
Liu, Ronghui
Ye, Yufang
Zhang, Shuqian
Fan, Bing
Diagnostic value of chest computed tomography images in adult Poland syndrome: a report of two cases
title Diagnostic value of chest computed tomography images in adult Poland syndrome: a report of two cases
title_full Diagnostic value of chest computed tomography images in adult Poland syndrome: a report of two cases
title_fullStr Diagnostic value of chest computed tomography images in adult Poland syndrome: a report of two cases
title_full_unstemmed Diagnostic value of chest computed tomography images in adult Poland syndrome: a report of two cases
title_short Diagnostic value of chest computed tomography images in adult Poland syndrome: a report of two cases
title_sort diagnostic value of chest computed tomography images in adult poland syndrome: a report of two cases
topic Case Reports
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8743957/
https://www.ncbi.nlm.nih.gov/pubmed/34994238
http://dx.doi.org/10.1177/03000605211069485
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