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A distinctive case of congenital midgut malrotation with volvulus in an adolescent female managed by Ladd's procedure - A case report

INTRODUCTION AND IMPORTANCE: Midgut Malrotation (MM) is a potentially fatal and rare congenital anomaly that results from an incomplete rotation of the bowel 270 degrees around the Superior Mesenteric Axis. Newborns are the most affected age group, nevertheless, adult malrotation can manifest, but i...

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Autores principales: Al Laham, Omar, Albrijawy, Reham, Ahmad, Issa, Atia, Fareed, Shaheen, Jack, Alaa Aldeen, Belal
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8749212/
https://www.ncbi.nlm.nih.gov/pubmed/34999472
http://dx.doi.org/10.1016/j.ijscr.2021.106752
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author Al Laham, Omar
Albrijawy, Reham
Ahmad, Issa
Atia, Fareed
Shaheen, Jack
Alaa Aldeen, Belal
author_facet Al Laham, Omar
Albrijawy, Reham
Ahmad, Issa
Atia, Fareed
Shaheen, Jack
Alaa Aldeen, Belal
author_sort Al Laham, Omar
collection PubMed
description INTRODUCTION AND IMPORTANCE: Midgut Malrotation (MM) is a potentially fatal and rare congenital anomaly that results from an incomplete rotation of the bowel 270 degrees around the Superior Mesenteric Axis. Newborns are the most affected age group, nevertheless, adult malrotation can manifest, but in a much rarer incidence rate. Clinical awareness must be present when faced with a surgical abdomen in an adolescent patient because this pathology can have several misleading signs and symptoms which may eclipse the true preoperative diagnosis and masquerade as another, and this could result in implementing a different therapeutic approach. Swift clinical informed judgments must be made and acted upon to limit the morbidity and mortality resultant from this pathology. CASE PRESENTATION: We present the case of a 15-year-old female, who was brought to our Emergency Department (ED) with a 5-day-history of biliary emesis which evolved into obstipation with continuous and excruciating abdominal pain. Computed Tomography (CT) scan indicated gastric and duodenal dilation in addition to a “Whirlpool sign”. Exploratory laparotomy was done, and a Ladd's procedure was performed. CLINICAL DISCUSSION: We treated our patient by performing Ladd's procedure and adhesiolysis. Diagnosis is conventionally established pre-/intraoperatively based on radiological imaging and clinical suspicion. Therapeutic methods for this pathology are primarily surgical in nature. CONCLUSION: Midgut Malrotation is a rare entity, thus, it is crucial to further study this type of clinical presentation and keep it in mind to be able to make an accurate diagnosis to reach the optimal outcome for patients who present with acute surgical abdomen.
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spelling pubmed-87492122022-01-13 A distinctive case of congenital midgut malrotation with volvulus in an adolescent female managed by Ladd's procedure - A case report Al Laham, Omar Albrijawy, Reham Ahmad, Issa Atia, Fareed Shaheen, Jack Alaa Aldeen, Belal Int J Surg Case Rep Case Report INTRODUCTION AND IMPORTANCE: Midgut Malrotation (MM) is a potentially fatal and rare congenital anomaly that results from an incomplete rotation of the bowel 270 degrees around the Superior Mesenteric Axis. Newborns are the most affected age group, nevertheless, adult malrotation can manifest, but in a much rarer incidence rate. Clinical awareness must be present when faced with a surgical abdomen in an adolescent patient because this pathology can have several misleading signs and symptoms which may eclipse the true preoperative diagnosis and masquerade as another, and this could result in implementing a different therapeutic approach. Swift clinical informed judgments must be made and acted upon to limit the morbidity and mortality resultant from this pathology. CASE PRESENTATION: We present the case of a 15-year-old female, who was brought to our Emergency Department (ED) with a 5-day-history of biliary emesis which evolved into obstipation with continuous and excruciating abdominal pain. Computed Tomography (CT) scan indicated gastric and duodenal dilation in addition to a “Whirlpool sign”. Exploratory laparotomy was done, and a Ladd's procedure was performed. CLINICAL DISCUSSION: We treated our patient by performing Ladd's procedure and adhesiolysis. Diagnosis is conventionally established pre-/intraoperatively based on radiological imaging and clinical suspicion. Therapeutic methods for this pathology are primarily surgical in nature. CONCLUSION: Midgut Malrotation is a rare entity, thus, it is crucial to further study this type of clinical presentation and keep it in mind to be able to make an accurate diagnosis to reach the optimal outcome for patients who present with acute surgical abdomen. Elsevier 2022-01-05 /pmc/articles/PMC8749212/ /pubmed/34999472 http://dx.doi.org/10.1016/j.ijscr.2021.106752 Text en © 2022 The Authors https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Case Report
Al Laham, Omar
Albrijawy, Reham
Ahmad, Issa
Atia, Fareed
Shaheen, Jack
Alaa Aldeen, Belal
A distinctive case of congenital midgut malrotation with volvulus in an adolescent female managed by Ladd's procedure - A case report
title A distinctive case of congenital midgut malrotation with volvulus in an adolescent female managed by Ladd's procedure - A case report
title_full A distinctive case of congenital midgut malrotation with volvulus in an adolescent female managed by Ladd's procedure - A case report
title_fullStr A distinctive case of congenital midgut malrotation with volvulus in an adolescent female managed by Ladd's procedure - A case report
title_full_unstemmed A distinctive case of congenital midgut malrotation with volvulus in an adolescent female managed by Ladd's procedure - A case report
title_short A distinctive case of congenital midgut malrotation with volvulus in an adolescent female managed by Ladd's procedure - A case report
title_sort distinctive case of congenital midgut malrotation with volvulus in an adolescent female managed by ladd's procedure - a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8749212/
https://www.ncbi.nlm.nih.gov/pubmed/34999472
http://dx.doi.org/10.1016/j.ijscr.2021.106752
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