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In Vitro and In Vivo Models to Study Nephropathic Cystinosis
The development over the past 50 years of a variety of cell lines and animal models has provided valuable tools to understand the pathophysiology of nephropathic cystinosis. Primary cultures from patient biopsies have been instrumental in determining the primary cause of cystine accumulation in the...
Autores principales: | Cheung, Pang Yuk, Harrison, Patrick T., Davidson, Alan J., Hollywood, Jennifer A. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2021
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8750259/ https://www.ncbi.nlm.nih.gov/pubmed/35011573 http://dx.doi.org/10.3390/cells11010006 |
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