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Nephropathic Cystinosis: Pathogenic Roles of Inflammation and Potential for New Therapies
The activation of several inflammatory pathways has recently been documented in patients and different cellular and animal models of nephropathic cystinosis. Upregulated inflammatory signals interact with many pathogenic aspects of the disease, such as enhanced oxidative stress, abnormal autophagy,...
Autores principales: | Elmonem, Mohamed A., Veys, Koenraad R. P., Prencipe, Giusi |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2022
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8773784/ https://www.ncbi.nlm.nih.gov/pubmed/35053306 http://dx.doi.org/10.3390/cells11020190 |
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