Cargando…

Fahr’s Syndrome Presenting As Pre-senile Dementia With Behavioral Abnormalities: A Rare Case Report

Fahr’s syndrome is a rare neurological disorder characterized by bilateral basal ganglia calcification. Calcification may also involve other brain areas like dentate nuclei of the cerebellum, thalamus, cerebral cortex, hippocampus, and subcortical white matter. Many cases of Fahr’s syndrome present...

Descripción completa

Detalles Bibliográficos
Autores principales: Ghogare, Ajinkya S, Nemade, Shyam
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8786577/
https://www.ncbi.nlm.nih.gov/pubmed/35106221
http://dx.doi.org/10.7759/cureus.20680
_version_ 1784639141141544960
author Ghogare, Ajinkya S
Nemade, Shyam
author_facet Ghogare, Ajinkya S
Nemade, Shyam
author_sort Ghogare, Ajinkya S
collection PubMed
description Fahr’s syndrome is a rare neurological disorder characterized by bilateral basal ganglia calcification. Calcification may also involve other brain areas like dentate nuclei of the cerebellum, thalamus, cerebral cortex, hippocampus, and subcortical white matter. Many cases of Fahr’s syndrome present with movement disorders, but may also present with dementia, psychiatric manifestations, and language difficulties. Fahr’s syndrome generally occurs secondary to metabolic abnormality mainly hypoparathyroidism. Fahr’s disease is another variant that is characterized by idiopathic bilateral calcification of basal ganglia in absence of any evident etiology. The present case report presented a rare case of Fahr’s syndrome secondary to hypoparathyroidism presenting with pre-senile dementia with behavioral abnormalities.
format Online
Article
Text
id pubmed-8786577
institution National Center for Biotechnology Information
language English
publishDate 2021
publisher Cureus
record_format MEDLINE/PubMed
spelling pubmed-87865772022-01-31 Fahr’s Syndrome Presenting As Pre-senile Dementia With Behavioral Abnormalities: A Rare Case Report Ghogare, Ajinkya S Nemade, Shyam Cureus Neurology Fahr’s syndrome is a rare neurological disorder characterized by bilateral basal ganglia calcification. Calcification may also involve other brain areas like dentate nuclei of the cerebellum, thalamus, cerebral cortex, hippocampus, and subcortical white matter. Many cases of Fahr’s syndrome present with movement disorders, but may also present with dementia, psychiatric manifestations, and language difficulties. Fahr’s syndrome generally occurs secondary to metabolic abnormality mainly hypoparathyroidism. Fahr’s disease is another variant that is characterized by idiopathic bilateral calcification of basal ganglia in absence of any evident etiology. The present case report presented a rare case of Fahr’s syndrome secondary to hypoparathyroidism presenting with pre-senile dementia with behavioral abnormalities. Cureus 2021-12-25 /pmc/articles/PMC8786577/ /pubmed/35106221 http://dx.doi.org/10.7759/cureus.20680 Text en Copyright © 2021, Ghogare et al. https://creativecommons.org/licenses/by/3.0/This is an open access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.
spellingShingle Neurology
Ghogare, Ajinkya S
Nemade, Shyam
Fahr’s Syndrome Presenting As Pre-senile Dementia With Behavioral Abnormalities: A Rare Case Report
title Fahr’s Syndrome Presenting As Pre-senile Dementia With Behavioral Abnormalities: A Rare Case Report
title_full Fahr’s Syndrome Presenting As Pre-senile Dementia With Behavioral Abnormalities: A Rare Case Report
title_fullStr Fahr’s Syndrome Presenting As Pre-senile Dementia With Behavioral Abnormalities: A Rare Case Report
title_full_unstemmed Fahr’s Syndrome Presenting As Pre-senile Dementia With Behavioral Abnormalities: A Rare Case Report
title_short Fahr’s Syndrome Presenting As Pre-senile Dementia With Behavioral Abnormalities: A Rare Case Report
title_sort fahr’s syndrome presenting as pre-senile dementia with behavioral abnormalities: a rare case report
topic Neurology
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8786577/
https://www.ncbi.nlm.nih.gov/pubmed/35106221
http://dx.doi.org/10.7759/cureus.20680
work_keys_str_mv AT ghogareajinkyas fahrssyndromepresentingaspreseniledementiawithbehavioralabnormalitiesararecasereport
AT nemadeshyam fahrssyndromepresentingaspreseniledementiawithbehavioralabnormalitiesararecasereport