Bilateral congenital stromal iris cyst with secondary glaucoma

PURPOSE: To report a case of bilateral congenital stromal iris cyst in a neonate. OBSERVATIONS: A one-month-old male child was brought with complaints of watering in both eyes and enlargement of the left eye since birth. Examination under anesthesia revealed an elevated IOP in both the eyes. The left eye had buphthalmos with hazy cornea and central corneal scarring. Ultrasound biomicroscopy revealed the presence of a stromal cyst in both the eyes and a cataractous lens in the left eye. While the right eye responded to topical glaucoma medications, the left eye continued to have a high IOP and hence, it was managed surgically. CONCLUSIONS AND IMPORTANCE: This rare case of bilateral stromal iris cyst in a neonate presented with a unique diagnostic and management challenge.