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Coblation debulking of a paediatric laryngeal plexiform neurofibroma: a pragmatic response to a rare tumour
Laryngeal neurofibroma is a rare but important differential diagnosis in a patient presenting with stridor. In paediatric patients, these lesions present a management conundrum: complete surgical resection is the established treatment of choice, but an aggressive approach can be detrimental to devel...
Autores principales: | , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Oxford University Press
2022
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8791663/ https://www.ncbi.nlm.nih.gov/pubmed/35096374 http://dx.doi.org/10.1093/jscr/rjab646 |
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author | Schuster-Bruce, James Kelly, Mairead Bernic, Ana Brar, Sabrina Barber, Joy Modayil, Prince |
author_facet | Schuster-Bruce, James Kelly, Mairead Bernic, Ana Brar, Sabrina Barber, Joy Modayil, Prince |
author_sort | Schuster-Bruce, James |
collection | PubMed |
description | Laryngeal neurofibroma is a rare but important differential diagnosis in a patient presenting with stridor. In paediatric patients, these lesions present a management conundrum: complete surgical resection is the established treatment of choice, but an aggressive approach can be detrimental to developing anatomy. We report the case of a plexiform neurofibroma affecting the right hemilarynx of a 3-year-old boy. Endoscopy revealed a large tumour, involving the right aryepiglottic fold and extending into the piriform sinus, ventricle and the false cord. Given the patient’s young age and the challenging tumour location, the lesion was debulked, rather than resected, using coblation (low-temperature plasma radiofrequency ablation). At 30 months follow-up, the neurofibroma has mildly increased in size—in line with expectations that these lesions exhibit slow growth throughout childhood—but there are no significant respiratory symptoms and there is no functional impairment. |
format | Online Article Text |
id | pubmed-8791663 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2022 |
publisher | Oxford University Press |
record_format | MEDLINE/PubMed |
spelling | pubmed-87916632022-01-27 Coblation debulking of a paediatric laryngeal plexiform neurofibroma: a pragmatic response to a rare tumour Schuster-Bruce, James Kelly, Mairead Bernic, Ana Brar, Sabrina Barber, Joy Modayil, Prince J Surg Case Rep Case Report Laryngeal neurofibroma is a rare but important differential diagnosis in a patient presenting with stridor. In paediatric patients, these lesions present a management conundrum: complete surgical resection is the established treatment of choice, but an aggressive approach can be detrimental to developing anatomy. We report the case of a plexiform neurofibroma affecting the right hemilarynx of a 3-year-old boy. Endoscopy revealed a large tumour, involving the right aryepiglottic fold and extending into the piriform sinus, ventricle and the false cord. Given the patient’s young age and the challenging tumour location, the lesion was debulked, rather than resected, using coblation (low-temperature plasma radiofrequency ablation). At 30 months follow-up, the neurofibroma has mildly increased in size—in line with expectations that these lesions exhibit slow growth throughout childhood—but there are no significant respiratory symptoms and there is no functional impairment. Oxford University Press 2022-01-26 /pmc/articles/PMC8791663/ /pubmed/35096374 http://dx.doi.org/10.1093/jscr/rjab646 Text en Published by Oxford University Press and JSCR Publishing Ltd. © The Author(s) 2022. https://creativecommons.org/licenses/by/4.0/This is an Open Access article distributed under the terms of the Creative Commons Attribution License (https://creativecommons.org/licenses/by/4.0/), which permits unrestricted reuse, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Schuster-Bruce, James Kelly, Mairead Bernic, Ana Brar, Sabrina Barber, Joy Modayil, Prince Coblation debulking of a paediatric laryngeal plexiform neurofibroma: a pragmatic response to a rare tumour |
title | Coblation debulking of a paediatric laryngeal plexiform neurofibroma: a pragmatic response to a rare tumour |
title_full | Coblation debulking of a paediatric laryngeal plexiform neurofibroma: a pragmatic response to a rare tumour |
title_fullStr | Coblation debulking of a paediatric laryngeal plexiform neurofibroma: a pragmatic response to a rare tumour |
title_full_unstemmed | Coblation debulking of a paediatric laryngeal plexiform neurofibroma: a pragmatic response to a rare tumour |
title_short | Coblation debulking of a paediatric laryngeal plexiform neurofibroma: a pragmatic response to a rare tumour |
title_sort | coblation debulking of a paediatric laryngeal plexiform neurofibroma: a pragmatic response to a rare tumour |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8791663/ https://www.ncbi.nlm.nih.gov/pubmed/35096374 http://dx.doi.org/10.1093/jscr/rjab646 |
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