Mixed connective tissue disease and idiopathic retroperitoneal fibrosis: A rare but important association

Idiopathic Retroperitoneal fibrosis (RPF) is a fibro-inflammatory disease. In patients with known mixed connective tissue disease (MCTD) it has rarely been described. Our case illustrates a unique presentation of RPF in a patient with MCTD. We emphasise possible links between the two disease process...

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Detalles Bibliográficos
Autores principales: Neerhut, Thomas, Mills, Alexander, Davies, Samuel, Rhee, Handoo
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2022
Materias:
Inflammation and Infection
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8801759/
https://www.ncbi.nlm.nih.gov/pubmed/35145871
http://dx.doi.org/10.1016/j.eucr.2022.102009
Descripción
Sumario:Idiopathic Retroperitoneal fibrosis (RPF) is a fibro-inflammatory disease. In patients with known mixed connective tissue disease (MCTD) it has rarely been described. Our case illustrates a unique presentation of RPF in a patient with MCTD. We emphasise possible links between the two disease processes and the high level of clinical suspicion required to make a diagnosis.

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