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Mixed connective tissue disease and idiopathic retroperitoneal fibrosis: A rare but important association

Idiopathic Retroperitoneal fibrosis (RPF) is a fibro-inflammatory disease. In patients with known mixed connective tissue disease (MCTD) it has rarely been described. Our case illustrates a unique presentation of RPF in a patient with MCTD. We emphasise possible links between the two disease process...

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Detalles Bibliográficos
Autores principales: Neerhut, Thomas, Mills, Alexander, Davies, Samuel, Rhee, Handoo
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8801759/
https://www.ncbi.nlm.nih.gov/pubmed/35145871
http://dx.doi.org/10.1016/j.eucr.2022.102009
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author Neerhut, Thomas
Mills, Alexander
Davies, Samuel
Rhee, Handoo
author_facet Neerhut, Thomas
Mills, Alexander
Davies, Samuel
Rhee, Handoo
author_sort Neerhut, Thomas
collection PubMed
description Idiopathic Retroperitoneal fibrosis (RPF) is a fibro-inflammatory disease. In patients with known mixed connective tissue disease (MCTD) it has rarely been described. Our case illustrates a unique presentation of RPF in a patient with MCTD. We emphasise possible links between the two disease processes and the high level of clinical suspicion required to make a diagnosis.
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spelling pubmed-88017592022-02-09 Mixed connective tissue disease and idiopathic retroperitoneal fibrosis: A rare but important association Neerhut, Thomas Mills, Alexander Davies, Samuel Rhee, Handoo Urol Case Rep Inflammation and Infection Idiopathic Retroperitoneal fibrosis (RPF) is a fibro-inflammatory disease. In patients with known mixed connective tissue disease (MCTD) it has rarely been described. Our case illustrates a unique presentation of RPF in a patient with MCTD. We emphasise possible links between the two disease processes and the high level of clinical suspicion required to make a diagnosis. Elsevier 2022-01-23 /pmc/articles/PMC8801759/ /pubmed/35145871 http://dx.doi.org/10.1016/j.eucr.2022.102009 Text en Crown Copyright © 2022 Published by Elsevier Inc. https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Inflammation and Infection
Neerhut, Thomas
Mills, Alexander
Davies, Samuel
Rhee, Handoo
Mixed connective tissue disease and idiopathic retroperitoneal fibrosis: A rare but important association
title Mixed connective tissue disease and idiopathic retroperitoneal fibrosis: A rare but important association
title_full Mixed connective tissue disease and idiopathic retroperitoneal fibrosis: A rare but important association
title_fullStr Mixed connective tissue disease and idiopathic retroperitoneal fibrosis: A rare but important association
title_full_unstemmed Mixed connective tissue disease and idiopathic retroperitoneal fibrosis: A rare but important association
title_short Mixed connective tissue disease and idiopathic retroperitoneal fibrosis: A rare but important association
title_sort mixed connective tissue disease and idiopathic retroperitoneal fibrosis: a rare but important association
topic Inflammation and Infection
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8801759/
https://www.ncbi.nlm.nih.gov/pubmed/35145871
http://dx.doi.org/10.1016/j.eucr.2022.102009
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