Sporadic Intradural Extramedullary Hemangioblastoma of Cauda Equina with Large Peritumoral Cyst—A Rare Presentation

Cauda equina intradural tumors commonly reported include ependymoma, schwannoma, neurofibroma, meningioma, and drop metastasis. Hemangioblastoma of the neural axis is a rare benign vascular tumor comprising only 1.6 to 6.4% of spinal tumors, and are usually associated with Von-Hippel Lindau disease....

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Autores principales: Thippeswamy, Pushpa B., Soundararajan, Dilip C. R., Kanna, Ríshi M., Kuna, Venkata S., Rajasekaran, Shanmuganathan
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Thieme Medical and Scientific Publishers Pvt. Ltd. 2022
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8817792/
https://www.ncbi.nlm.nih.gov/pubmed/35136529
http://dx.doi.org/10.1055/s-0041-1741047
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author Thippeswamy, Pushpa B.
Soundararajan, Dilip C. R.
Kanna, Ríshi M.
Kuna, Venkata S.
Rajasekaran, Shanmuganathan
author_facet Thippeswamy, Pushpa B.
Soundararajan, Dilip C. R.
Kanna, Ríshi M.
Kuna, Venkata S.
Rajasekaran, Shanmuganathan
author_sort Thippeswamy, Pushpa B.
collection PubMed
description Cauda equina intradural tumors commonly reported include ependymoma, schwannoma, neurofibroma, meningioma, and drop metastasis. Hemangioblastoma of the neural axis is a rare benign vascular tumor comprising only 1.6 to 6.4% of spinal tumors, and are usually associated with Von-Hippel Lindau disease. Sporadic intradural extramedullary hemangioblastoma involving cauda equina is very rare with only countable reports, and the presence of peritumoral cyst has been reported only once. We report one such case of hemangioblastoma with a large peritumoral cyst, which was diagnosed radiologically and confirmed by histopathology following surgical excision. Pertinent radiological characteristics, diagnostic clues, treatment, and surgical outcomes are discussed.
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spelling pubmed-88177922022-02-07 Sporadic Intradural Extramedullary Hemangioblastoma of Cauda Equina with Large Peritumoral Cyst—A Rare Presentation Thippeswamy, Pushpa B. Soundararajan, Dilip C. R. Kanna, Ríshi M. Kuna, Venkata S. Rajasekaran, Shanmuganathan Indian J Radiol Imaging Cauda equina intradural tumors commonly reported include ependymoma, schwannoma, neurofibroma, meningioma, and drop metastasis. Hemangioblastoma of the neural axis is a rare benign vascular tumor comprising only 1.6 to 6.4% of spinal tumors, and are usually associated with Von-Hippel Lindau disease. Sporadic intradural extramedullary hemangioblastoma involving cauda equina is very rare with only countable reports, and the presence of peritumoral cyst has been reported only once. We report one such case of hemangioblastoma with a large peritumoral cyst, which was diagnosed radiologically and confirmed by histopathology following surgical excision. Pertinent radiological characteristics, diagnostic clues, treatment, and surgical outcomes are discussed. Thieme Medical and Scientific Publishers Pvt. Ltd. 2022-01-10 /pmc/articles/PMC8817792/ /pubmed/35136529 http://dx.doi.org/10.1055/s-0041-1741047 Text en Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. ( https://creativecommons.org/licenses/by-nc-nd/4.0/ ) https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open-access article distributed under the terms of the Creative Commons Attribution-NonCommercial-NoDerivatives License, which permits unrestricted reproduction and distribution, for non-commercial purposes only; and use and reproduction, but not distribution, of adapted material for non-commercial purposes only, provided the original work is properly cited.
spellingShingle Thippeswamy, Pushpa B.
Soundararajan, Dilip C. R.
Kanna, Ríshi M.
Kuna, Venkata S.
Rajasekaran, Shanmuganathan
Sporadic Intradural Extramedullary Hemangioblastoma of Cauda Equina with Large Peritumoral Cyst—A Rare Presentation
title Sporadic Intradural Extramedullary Hemangioblastoma of Cauda Equina with Large Peritumoral Cyst—A Rare Presentation
title_full Sporadic Intradural Extramedullary Hemangioblastoma of Cauda Equina with Large Peritumoral Cyst—A Rare Presentation
title_fullStr Sporadic Intradural Extramedullary Hemangioblastoma of Cauda Equina with Large Peritumoral Cyst—A Rare Presentation
title_full_unstemmed Sporadic Intradural Extramedullary Hemangioblastoma of Cauda Equina with Large Peritumoral Cyst—A Rare Presentation
title_short Sporadic Intradural Extramedullary Hemangioblastoma of Cauda Equina with Large Peritumoral Cyst—A Rare Presentation
title_sort sporadic intradural extramedullary hemangioblastoma of cauda equina with large peritumoral cyst—a rare presentation
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8817792/
https://www.ncbi.nlm.nih.gov/pubmed/35136529
http://dx.doi.org/10.1055/s-0041-1741047
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