Cargando…

Langerhan's Cell Histiocytosis of Sphenoid Sinus causing Vision Loss: A Case Report

Langerhan's cell histiocytosis is an uncontrolled proliferation of dendritic cells. The involvement of skull base is rare. Variable clinical presentation and multi organ involvement often warrant a multidisciplinary approach for a successful diagnosis. We are reporting a case of 16-year-old mal...

Descripción completa

Detalles Bibliográficos
Autores principales: Mani, Suresh, Thomas, Regi, Mathew, John, Michael, Rajiv
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Journal of the Nepal Medical Association 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8827521/
http://dx.doi.org/10.31729/jnma.3959
_version_ 1784647647815008256
author Mani, Suresh
Thomas, Regi
Mathew, John
Michael, Rajiv
author_facet Mani, Suresh
Thomas, Regi
Mathew, John
Michael, Rajiv
author_sort Mani, Suresh
collection PubMed
description Langerhan's cell histiocytosis is an uncontrolled proliferation of dendritic cells. The involvement of skull base is rare. Variable clinical presentation and multi organ involvement often warrant a multidisciplinary approach for a successful diagnosis. We are reporting a case of 16-year-old male with sphenoid sinus Langerhan's cell histiocytosis which presented as a sudden and painless loss of vision. It is a rare entity in the diagnosis of blindness. Delayed diagnosis and treatment can result in serious complications. The radiological features and management options are discussed with a review of the pertinent literature.
format Online
Article
Text
id pubmed-8827521
institution National Center for Biotechnology Information
language English
publishDate 2019
publisher Journal of the Nepal Medical Association
record_format MEDLINE/PubMed
spelling pubmed-88275212022-03-01 Langerhan's Cell Histiocytosis of Sphenoid Sinus causing Vision Loss: A Case Report Mani, Suresh Thomas, Regi Mathew, John Michael, Rajiv JNMA J Nepal Med Assoc Case Report Langerhan's cell histiocytosis is an uncontrolled proliferation of dendritic cells. The involvement of skull base is rare. Variable clinical presentation and multi organ involvement often warrant a multidisciplinary approach for a successful diagnosis. We are reporting a case of 16-year-old male with sphenoid sinus Langerhan's cell histiocytosis which presented as a sudden and painless loss of vision. It is a rare entity in the diagnosis of blindness. Delayed diagnosis and treatment can result in serious complications. The radiological features and management options are discussed with a review of the pertinent literature. Journal of the Nepal Medical Association 2019-08 2019-08-31 /pmc/articles/PMC8827521/ http://dx.doi.org/10.31729/jnma.3959 Text en © The Author(s) 2018. https://creativecommons.org/licenses/by/4.0/This is an Open-Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/4.0) which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Mani, Suresh
Thomas, Regi
Mathew, John
Michael, Rajiv
Langerhan's Cell Histiocytosis of Sphenoid Sinus causing Vision Loss: A Case Report
title Langerhan's Cell Histiocytosis of Sphenoid Sinus causing Vision Loss: A Case Report
title_full Langerhan's Cell Histiocytosis of Sphenoid Sinus causing Vision Loss: A Case Report
title_fullStr Langerhan's Cell Histiocytosis of Sphenoid Sinus causing Vision Loss: A Case Report
title_full_unstemmed Langerhan's Cell Histiocytosis of Sphenoid Sinus causing Vision Loss: A Case Report
title_short Langerhan's Cell Histiocytosis of Sphenoid Sinus causing Vision Loss: A Case Report
title_sort langerhan's cell histiocytosis of sphenoid sinus causing vision loss: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8827521/
http://dx.doi.org/10.31729/jnma.3959
work_keys_str_mv AT manisuresh langerhanscellhistiocytosisofsphenoidsinuscausingvisionlossacasereport
AT thomasregi langerhanscellhistiocytosisofsphenoidsinuscausingvisionlossacasereport
AT mathewjohn langerhanscellhistiocytosisofsphenoidsinuscausingvisionlossacasereport
AT michaelrajiv langerhanscellhistiocytosisofsphenoidsinuscausingvisionlossacasereport