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Early Morphological Changes of the Rectus Femoris Muscle and Deep Fascia in Ullrich Congenital Muscular Dystrophy

Ullrich congenital muscular dystrophy (UCMD) is a severe form of muscular dystrophy caused by the loss of function of collagen VI, a critical component of the muscle-tendon matrix. Magnetic resonance imaging of UCMD patients’ muscles shows a peculiar rim of abnormal signal at the periphery of each m...

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Detalles Bibliográficos
Autores principales:	Sabatelli, Patrizia, Merlini, Luciano, Di Martino, Alberto, Cenni, Vittoria, Faldini, Cesare
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2022
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8834967/ https://www.ncbi.nlm.nih.gov/pubmed/35162283 http://dx.doi.org/10.3390/ijerph19031252

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