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Assays of CFTR Function In Vitro, Ex Vivo and In Vivo

Cystic fibrosis, a multi-organ genetic disease, is characterized by abnormal function of the cystic fibrosis transmembrane conductance regulator (CFTR) protein, a chloride channel at the apical membrane of several epithelia. In recent years, therapeutic strategies have been developed to correct the...

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Detalles Bibliográficos
Autores principales:	Ramalho, Anabela S., Boon, Mieke, Proesmans, Marijke, Vermeulen, François, Carlon, Marianne S., De Boeck, Kris
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2022
Materias:	Review
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8836180/ https://www.ncbi.nlm.nih.gov/pubmed/35163362 http://dx.doi.org/10.3390/ijms23031437

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