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A thrombopoietin receptor agonist to rescue an unusual platelet transfusion-induced reaction in a p.V1316M-associated von Willebrand disease type 2B patient
This report describes the first case of splenic injury in a patient with p.V1316M-associated von Willebrand disease type 2B (VWD2B) with chronic thrombocytopenia, successfully treated with nonoperative management including von Willebrand factor (VWF) replacement therapy, and platelet transfusions re...
Autores principales: | Casari, Caterina, Favier, Remi, Legendre, Paulette, Kauskot, Alexandre, Adam, Frederic, Picard, Veronique, Lenting, Peter T., Denis, Cecile V., Proulle, Valerie |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
SAGE Publications
2022
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8855378/ https://www.ncbi.nlm.nih.gov/pubmed/35186246 http://dx.doi.org/10.1177/20406207221076812 |
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