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Isoprostanoid Plasma Levels Are Relevant to Cerebral Adrenoleukodystrophy Disease

Cerebral adrenoleukodystrophy (ALD) is a rare neuroinflammatory disorder characterized by progressive demyelination. Mutations within the ABCD1 gene result in very long-chain fatty acid (VLCFA) accumulation within the peroxisome, particularly in the brain. While this VLCFA accumulation is known to b...

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Detalles Bibliográficos
Autores principales:	Signorini, Cinzia, De Felice, Claudio, Durand, Thierry, Galano, Jean-Marie, Oger, Camille, Leoncini, Silvia, Hayek, Joussef, Lee, Jetty Chung-Yung, Lund, Troy C., Orchard, Paul J.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2022
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8874514/ https://www.ncbi.nlm.nih.gov/pubmed/35207434 http://dx.doi.org/10.3390/life12020146

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