Cargando…
Vitamin D and Calcium Supplementation Accelerate Vascular Calcification in a Model of Pseudoxanthoma Elasticum
Arterial calcification is a common feature of pseudoxanthoma elasticum (PXE), a disease characterized by ABCC6 mutations, inducing a deficiency in pyrophosphate, a key inhibitor of calcium phosphate crystallization in arteries. Methods: we analyzed whether long-term exposure of Abcc6(−/−) mice (a mu...
Autores principales: | Bouderlique, Elise, Tang, Ellie, Zaworski, Jeremy, Coudert, Amélie, Bazin, Dominique, Borondics, Ferenc, Haymann, Jean-Philippe, Leftheriotis, Georges, Martin, Ludovic, Daudon, Michel, Letavernier, Emmanuel |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2022
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8878394/ https://www.ncbi.nlm.nih.gov/pubmed/35216422 http://dx.doi.org/10.3390/ijms23042302 |
Ejemplares similares
-
Pseudoxanthoma Elasticum, Kidney Stones and Pyrophosphate: From a Rare Disease to Urolithiasis and Vascular Calcifications
por: Letavernier, Emmanuel, et al.
Publicado: (2019) -
Minocycline Counteracts Ectopic Calcification in a Murine Model of Pseudoxanthoma Elasticum: A Proof-of-Concept Study
por: Bouderlique, Elise, et al.
Publicado: (2022) -
The Contribution of Arterial Calcification to Peripheral Arterial Disease in Pseudoxanthoma Elasticum
por: Leftheriotis, Georges, et al.
Publicado: (2014) -
Relationships between Plasma Pyrophosphate, Vascular Calcification and Clinical Severity in Patients Affected by Pseudoxanthoma Elasticum
por: Leftheriotis, Georges, et al.
Publicado: (2022) -
Evidence of Cardiovascular Calcification and Fibrosis in Pseudoxanthoma Elasticum Mouse Models Subjected to DOCA-Salt Hypertension
por: Omarjee, Loukman, et al.
Publicado: (2019)