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Incidental Intercostal Intramuscular Myxoma With Fibrous Dysplasia in a Patient With Mazabraud’s and McCune Albright Syndromes
Intramuscular myxoma is a rare entity that may present as single or multiple lesions in patients with Mazabraud’s syndrome and is characterized by intramuscular myxomas with fibrous dysplasia. Though intramuscular myxomas occur in large muscle groups, they can very rarely occur in the chest wall. We...
Autores principales: | , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Cureus
2022
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8898071/ https://www.ncbi.nlm.nih.gov/pubmed/35265436 http://dx.doi.org/10.7759/cureus.22869 |
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author | Tejani, Ali S Kukkar, Vishal |
author_facet | Tejani, Ali S Kukkar, Vishal |
author_sort | Tejani, Ali S |
collection | PubMed |
description | Intramuscular myxoma is a rare entity that may present as single or multiple lesions in patients with Mazabraud’s syndrome and is characterized by intramuscular myxomas with fibrous dysplasia. Though intramuscular myxomas occur in large muscle groups, they can very rarely occur in the chest wall. We present the case of a 41-year-old woman with an incidentally discovered intercostal mass on magnetic resonance cholangiopancreatography (MRCP). Repeat MRI demonstrated a lobulated, T2-hyperintense intercostal lesion and demonstrated adjacent fibrous dysplasia of the ribs, consistent with the patient’s history of Mazabraud's and McCune Albright syndromes. Histopathological exam following surgical resection confirmed a diagnosis of intramuscular myxoma without the presence of sarcomatous changes. Though small, slow-growing intramuscular myxomas may be observed with conservative management in the absence of significant symptoms, surgical resection is warranted to prevent complications such as osseous erosion or nerve impingement. |
format | Online Article Text |
id | pubmed-8898071 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2022 |
publisher | Cureus |
record_format | MEDLINE/PubMed |
spelling | pubmed-88980712022-03-08 Incidental Intercostal Intramuscular Myxoma With Fibrous Dysplasia in a Patient With Mazabraud’s and McCune Albright Syndromes Tejani, Ali S Kukkar, Vishal Cureus Radiology Intramuscular myxoma is a rare entity that may present as single or multiple lesions in patients with Mazabraud’s syndrome and is characterized by intramuscular myxomas with fibrous dysplasia. Though intramuscular myxomas occur in large muscle groups, they can very rarely occur in the chest wall. We present the case of a 41-year-old woman with an incidentally discovered intercostal mass on magnetic resonance cholangiopancreatography (MRCP). Repeat MRI demonstrated a lobulated, T2-hyperintense intercostal lesion and demonstrated adjacent fibrous dysplasia of the ribs, consistent with the patient’s history of Mazabraud's and McCune Albright syndromes. Histopathological exam following surgical resection confirmed a diagnosis of intramuscular myxoma without the presence of sarcomatous changes. Though small, slow-growing intramuscular myxomas may be observed with conservative management in the absence of significant symptoms, surgical resection is warranted to prevent complications such as osseous erosion or nerve impingement. Cureus 2022-03-05 /pmc/articles/PMC8898071/ /pubmed/35265436 http://dx.doi.org/10.7759/cureus.22869 Text en Copyright © 2022, Tejani et al. https://creativecommons.org/licenses/by/3.0/This is an open access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited. |
spellingShingle | Radiology Tejani, Ali S Kukkar, Vishal Incidental Intercostal Intramuscular Myxoma With Fibrous Dysplasia in a Patient With Mazabraud’s and McCune Albright Syndromes |
title | Incidental Intercostal Intramuscular Myxoma With Fibrous Dysplasia in a Patient With Mazabraud’s and McCune Albright Syndromes |
title_full | Incidental Intercostal Intramuscular Myxoma With Fibrous Dysplasia in a Patient With Mazabraud’s and McCune Albright Syndromes |
title_fullStr | Incidental Intercostal Intramuscular Myxoma With Fibrous Dysplasia in a Patient With Mazabraud’s and McCune Albright Syndromes |
title_full_unstemmed | Incidental Intercostal Intramuscular Myxoma With Fibrous Dysplasia in a Patient With Mazabraud’s and McCune Albright Syndromes |
title_short | Incidental Intercostal Intramuscular Myxoma With Fibrous Dysplasia in a Patient With Mazabraud’s and McCune Albright Syndromes |
title_sort | incidental intercostal intramuscular myxoma with fibrous dysplasia in a patient with mazabraud’s and mccune albright syndromes |
topic | Radiology |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8898071/ https://www.ncbi.nlm.nih.gov/pubmed/35265436 http://dx.doi.org/10.7759/cureus.22869 |
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