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Frontalis Suspension in Muscular Dystrophy: 16-years Follow-up

Acquired eyelid ptosis in adults, with complete loss of levator palpebrae superiosis function, can be a challenging problem to diagnose and treat. A 48-year-old woman with chronic bilateral severe blepharoptosis of 10 years duration is presented, whose neurological investigations excluded myasthenia...

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Autor principal: Abdulrauf, Badr M. I.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Lippincott Williams & Wilkins 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8939913/
https://www.ncbi.nlm.nih.gov/pubmed/35356040
http://dx.doi.org/10.1097/GOX.0000000000004225
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author Abdulrauf, Badr M. I.
author_facet Abdulrauf, Badr M. I.
author_sort Abdulrauf, Badr M. I.
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description Acquired eyelid ptosis in adults, with complete loss of levator palpebrae superiosis function, can be a challenging problem to diagnose and treat. A 48-year-old woman with chronic bilateral severe blepharoptosis of 10 years duration is presented, whose neurological investigations excluded myasthenia gravis. The patient was preliminarily diagnosed with chronic progressive external ophthalmoplegia. The levator excursion was negligible, and a frontalis suspension procedure was considered using a conventional autogenous fascia lata graft. An optimal outcome was achieved with over 16-years follow-up. Although the patient was healthy otherwise upon first presentation, 10 years later, she developed other neurologic manifestations, including dysphagia and oral dryness. The fact that blepharoptosis did not recur over the years in this case differentiates an oculo-pharyngeal type of muscular dystrophy in this patient from other types and from the more frequent condition of chronic progressive external ophthalmoplegia.
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spelling pubmed-89399132022-03-29 Frontalis Suspension in Muscular Dystrophy: 16-years Follow-up Abdulrauf, Badr M. I. Plast Reconstr Surg Glob Open Reconstructive Acquired eyelid ptosis in adults, with complete loss of levator palpebrae superiosis function, can be a challenging problem to diagnose and treat. A 48-year-old woman with chronic bilateral severe blepharoptosis of 10 years duration is presented, whose neurological investigations excluded myasthenia gravis. The patient was preliminarily diagnosed with chronic progressive external ophthalmoplegia. The levator excursion was negligible, and a frontalis suspension procedure was considered using a conventional autogenous fascia lata graft. An optimal outcome was achieved with over 16-years follow-up. Although the patient was healthy otherwise upon first presentation, 10 years later, she developed other neurologic manifestations, including dysphagia and oral dryness. The fact that blepharoptosis did not recur over the years in this case differentiates an oculo-pharyngeal type of muscular dystrophy in this patient from other types and from the more frequent condition of chronic progressive external ophthalmoplegia. Lippincott Williams & Wilkins 2022-03-22 /pmc/articles/PMC8939913/ /pubmed/35356040 http://dx.doi.org/10.1097/GOX.0000000000004225 Text en Copyright © 2022 The Author. Published by Wolters Kluwer Health, Inc. on behalf of The American Society of Plastic Surgeons. https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open-access article distributed under the terms of the Creative Commons Attribution-Non Commercial-No Derivatives License 4.0 (CCBY-NC-ND) (https://creativecommons.org/licenses/by-nc-nd/4.0/) , where it is permissible to download and share the work provided it is properly cited. The work cannot be changed in any way or used commercially without permission from the journal.
spellingShingle Reconstructive
Abdulrauf, Badr M. I.
Frontalis Suspension in Muscular Dystrophy: 16-years Follow-up
title Frontalis Suspension in Muscular Dystrophy: 16-years Follow-up
title_full Frontalis Suspension in Muscular Dystrophy: 16-years Follow-up
title_fullStr Frontalis Suspension in Muscular Dystrophy: 16-years Follow-up
title_full_unstemmed Frontalis Suspension in Muscular Dystrophy: 16-years Follow-up
title_short Frontalis Suspension in Muscular Dystrophy: 16-years Follow-up
title_sort frontalis suspension in muscular dystrophy: 16-years follow-up
topic Reconstructive
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8939913/
https://www.ncbi.nlm.nih.gov/pubmed/35356040
http://dx.doi.org/10.1097/GOX.0000000000004225
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