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Preserved Left Ventricular Function despite Myocardial Fibrosis and Myopathy in the Dystrophin-Deficient D2.B10-Dmd(mdx)/J Mouse

Duchenne muscular dystrophy involves an absence of dystrophin, a cytoskeletal protein which supports cell structural integrity and scaffolding for signalling molecules in myocytes. Affected individuals experience progressive muscle degeneration that leads to irreversible loss of ambulation and respi...

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Detalles Bibliográficos
Autores principales:	Hayes, Holly M., Angerosa, Julie, Piers, Adam T., White, Jason D., Koleff, Jane, Thurgood, Madeline, Moody, Jessica, Cheung, Michael M., Pepe, Salvatore
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Hindawi 2022
Materias:	Research Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8942668/ https://www.ncbi.nlm.nih.gov/pubmed/35340200 http://dx.doi.org/10.1155/2022/5362115

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