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Autoimmune pulmonary alveolar proteinosis in children

In childhood, a multitude of causes lead to pulmonary alveolar proteinosis (PAP), an excessive surfactant accumulation in the alveolar space, limiting gas exchange. Autoantibodies against granulocyte–macrophage colony-stimulating factor (GM-CSF) causing autoimmune PAP, the principal aetiology in adu...

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Detalles Bibliográficos
Autores principales:	Griese, Matthias, Panagiotou, Panagiota, Manali, Effrosyni D., Stahl, Mirjam, Schwerk, Nicolaus, Costa, Vanessa, Douros, Konstantinos, Kallieri, Maria, Urbantat, Ruth Maria, von Bernuth, Horst, Kolilekas, Lykourgos, Morais, Lurdes, Ramos, Ana, Landwehr, Kerstin, Knoflach, Katrin, Gothe, Florian, Reiter, Karl, Papaevangelou, Vassiliki, Kaditis, Athanasios G., Kanaka-Gantenbein, Christina, Papiris, Spyros A.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	European Respiratory Society 2022
Materias:	Original Research Articles
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8943280/ https://www.ncbi.nlm.nih.gov/pubmed/35350279 http://dx.doi.org/10.1183/23120541.00701-2021

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