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Clinical Presentation of Left Ventricular Noncompaction Cardiomyopathy and Bradycardia in Three Families Carrying HCN4 Pathogenic Variants

Background: Left ventricular noncompaction (LVNC) is a genetically and phenotypically heterogeneous cardiomyopathy in which myocardium consists of two, distinct compacted and noncompacted layers, and prominent ventricular trabeculations and deep intertrabecular recesses are present. LVNC is associat...

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Detalles Bibliográficos
Autores principales:	Paszkowska, Agata, Piekutowska-Abramczuk, Dorota, Ciara, Elżbieta, Mirecka-Rola, Alicja, Brzezinska, Monika, Wicher, Dorota, Kostrzewa, Grażyna, Sarnecki, Jędrzej, Ziółkowska, Lidia
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2022
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8949387/ https://www.ncbi.nlm.nih.gov/pubmed/35328031 http://dx.doi.org/10.3390/genes13030477

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