Successful Surgical Repair of Type A Acute Aortic Dissection in a Patient with Vascular Ehlers–Danlos Syndrome

Surgery for vascular complications of a patient with vascular Ehlers–Danlos syndrome (vEDS) is challenging due to the fragility of the associated tissues. In this study, we present a type A acute aortic dissection case in a patient with vEDS successfully treated via total arch replacement. A 42-year...

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Autores principales: Mori, Kousuke, Ishii, Hirohito, Sakaguchi, Shuhei, Sakurahara, Daichi, Iwasaki, Ayaka, Furukawa, Koji
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Japanese College of Angiology / The Japanese Society for Vascular Surgery / Japanese Society of Phlebology 2022
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8958401/
https://www.ncbi.nlm.nih.gov/pubmed/35432645
http://dx.doi.org/10.3400/avd.cr.21-00122
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author Mori, Kousuke
Ishii, Hirohito
Sakaguchi, Shuhei
Sakurahara, Daichi
Iwasaki, Ayaka
Furukawa, Koji
author_facet Mori, Kousuke
Ishii, Hirohito
Sakaguchi, Shuhei
Sakurahara, Daichi
Iwasaki, Ayaka
Furukawa, Koji
author_sort Mori, Kousuke
collection PubMed
description Surgery for vascular complications of a patient with vascular Ehlers–Danlos syndrome (vEDS) is challenging due to the fragility of the associated tissues. In this study, we present a type A acute aortic dissection case in a patient with vEDS successfully treated via total arch replacement. A 42-year-old woman was transferred to our hospital 10 days after the onset of symptoms and underwent emergency surgery. Intraoperative findings revealed severe inflammatory changes without tissue fragility that is distinctive of vEDS. The postoperative course was uneventful except for left recurrent laryngeal nerve palsy, and 24 months after the operation, the patient has remained free from any arterial event.
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spelling pubmed-89584012022-04-14 Successful Surgical Repair of Type A Acute Aortic Dissection in a Patient with Vascular Ehlers–Danlos Syndrome Mori, Kousuke Ishii, Hirohito Sakaguchi, Shuhei Sakurahara, Daichi Iwasaki, Ayaka Furukawa, Koji Ann Vasc Dis Case Report Surgery for vascular complications of a patient with vascular Ehlers–Danlos syndrome (vEDS) is challenging due to the fragility of the associated tissues. In this study, we present a type A acute aortic dissection case in a patient with vEDS successfully treated via total arch replacement. A 42-year-old woman was transferred to our hospital 10 days after the onset of symptoms and underwent emergency surgery. Intraoperative findings revealed severe inflammatory changes without tissue fragility that is distinctive of vEDS. The postoperative course was uneventful except for left recurrent laryngeal nerve palsy, and 24 months after the operation, the patient has remained free from any arterial event. Japanese College of Angiology / The Japanese Society for Vascular Surgery / Japanese Society of Phlebology 2022-03-25 /pmc/articles/PMC8958401/ /pubmed/35432645 http://dx.doi.org/10.3400/avd.cr.21-00122 Text en © 2022 The Editorial Committee of Annals of Vascular Diseases. https://creativecommons.org/licenses/by/2.5/This article is distributed under the terms of the Creative Commons Attribution License, which permits use, distribution, and reproduction in any medium, provided the credit of the original work, a link to the license, and indication of any change are properly given, and the original work is not used for commercial purposes. Remixed or transformed contributions must be distributed under the same license as the original.
spellingShingle Case Report
Mori, Kousuke
Ishii, Hirohito
Sakaguchi, Shuhei
Sakurahara, Daichi
Iwasaki, Ayaka
Furukawa, Koji
Successful Surgical Repair of Type A Acute Aortic Dissection in a Patient with Vascular Ehlers–Danlos Syndrome
title Successful Surgical Repair of Type A Acute Aortic Dissection in a Patient with Vascular Ehlers–Danlos Syndrome
title_full Successful Surgical Repair of Type A Acute Aortic Dissection in a Patient with Vascular Ehlers–Danlos Syndrome
title_fullStr Successful Surgical Repair of Type A Acute Aortic Dissection in a Patient with Vascular Ehlers–Danlos Syndrome
title_full_unstemmed Successful Surgical Repair of Type A Acute Aortic Dissection in a Patient with Vascular Ehlers–Danlos Syndrome
title_short Successful Surgical Repair of Type A Acute Aortic Dissection in a Patient with Vascular Ehlers–Danlos Syndrome
title_sort successful surgical repair of type a acute aortic dissection in a patient with vascular ehlers–danlos syndrome
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8958401/
https://www.ncbi.nlm.nih.gov/pubmed/35432645
http://dx.doi.org/10.3400/avd.cr.21-00122
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