Cargando…
Drosophila as a Model of Unconventional Translation in Spinocerebellar Ataxia Type 3
RNA toxicity contributes to diseases caused by anomalous nucleotide repeat expansions. Recent work demonstrated RNA-based toxicity from repeat-associated, non-AUG-initiated translation (RAN translation). RAN translation occurs around long nucleotide repeats that form hairpin loops, allowing for tran...
Autores principales: | Johnson, Sean L., Prifti, Matthew V., Sujkowski, Alyson, Libohova, Kozeta, Blount, Jessica R., Hong, Luke, Tsou, Wei-Ling, Todi, Sokol V. |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2022
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8997593/ https://www.ncbi.nlm.nih.gov/pubmed/35406787 http://dx.doi.org/10.3390/cells11071223 |
Ejemplares similares
-
Targeting the VCP-binding motif of ataxin-3 improves phenotypes in Drosophila models of Spinocerebellar Ataxia Type 3
por: Johnson, Sean L., et al.
Publicado: (2021) -
Ubiquitin-binding site 1 of pathogenic ataxin-3 regulates its toxicity in Drosophila models of Spinocerebellar Ataxia Type 3
por: Prifti, Matthew V., et al.
Publicado: (2023) -
Phenotypic defects from the expression of wild-type and pathogenic TATA-binding proteins in new Drosophila models of Spinocerebellar Ataxia Type 17
por: Patel, Nikhil, et al.
Publicado: (2023) -
Progressive degeneration in a new Drosophila model of Spinocerebellar Ataxia type 7
por: Sujkowski, Alyson L., et al.
Publicado: (2023) -
Endurance exercise ameliorates phenotypes in Drosophila models of spinocerebellar ataxias
por: Sujkowski, Alyson, et al.
Publicado: (2022)