Anesthetic Management in a Case of MURCS Syndrome

MURCS syndrome is a more severe form of Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome, an acronym meaning aplasia/hypoplasia of Müllerian ducts (MU), congenital renal agenesis/ectopia (R), and cervical somite dysplasia (CS). A common presentation is primary amenorrhea in adolescent females. An anes...

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Autores principales: Rekha, J. R., Arora, Poonam, Arora, Rajnish Kumar, Arora, Monica
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer - Medknow 2021
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9004267/
https://www.ncbi.nlm.nih.gov/pubmed/35422543
http://dx.doi.org/10.4103/aer.aer_137_21
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author Rekha, J. R.
Arora, Poonam
Arora, Rajnish Kumar
Arora, Monica
author_facet Rekha, J. R.
Arora, Poonam
Arora, Rajnish Kumar
Arora, Monica
author_sort Rekha, J. R.
collection PubMed
description MURCS syndrome is a more severe form of Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome, an acronym meaning aplasia/hypoplasia of Müllerian ducts (MU), congenital renal agenesis/ectopia (R), and cervical somite dysplasia (CS). A common presentation is primary amenorrhea in adolescent females. An anesthetist must consider the benefits and limitations of both regional and general anesthesia for these patients based on site of surgery and severity of malformations. We report successful anesthetic management of a 21-year-old female with MURCS syndrome scheduled for a creation of neovagina under spinal anesthesia using ultrasound guidance.
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spelling pubmed-90042672022-04-13 Anesthetic Management in a Case of MURCS Syndrome Rekha, J. R. Arora, Poonam Arora, Rajnish Kumar Arora, Monica Anesth Essays Res Case Report MURCS syndrome is a more severe form of Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome, an acronym meaning aplasia/hypoplasia of Müllerian ducts (MU), congenital renal agenesis/ectopia (R), and cervical somite dysplasia (CS). A common presentation is primary amenorrhea in adolescent females. An anesthetist must consider the benefits and limitations of both regional and general anesthesia for these patients based on site of surgery and severity of malformations. We report successful anesthetic management of a 21-year-old female with MURCS syndrome scheduled for a creation of neovagina under spinal anesthesia using ultrasound guidance. Wolters Kluwer - Medknow 2021 2022-03-01 /pmc/articles/PMC9004267/ /pubmed/35422543 http://dx.doi.org/10.4103/aer.aer_137_21 Text en Copyright: © 2022 Anesthesia: Essays and Researches https://creativecommons.org/licenses/by-nc-sa/4.0/This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms.
spellingShingle Case Report
Rekha, J. R.
Arora, Poonam
Arora, Rajnish Kumar
Arora, Monica
Anesthetic Management in a Case of MURCS Syndrome
title Anesthetic Management in a Case of MURCS Syndrome
title_full Anesthetic Management in a Case of MURCS Syndrome
title_fullStr Anesthetic Management in a Case of MURCS Syndrome
title_full_unstemmed Anesthetic Management in a Case of MURCS Syndrome
title_short Anesthetic Management in a Case of MURCS Syndrome
title_sort anesthetic management in a case of murcs syndrome
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9004267/
https://www.ncbi.nlm.nih.gov/pubmed/35422543
http://dx.doi.org/10.4103/aer.aer_137_21
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