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Case Report: Diagnostic and Therapeutic Challenges in Severe Mechanobullous Epidermolysis Bullosa Acquisita

Collagen VII is the main constituent of the anchoring fibrils, important adhesive structures that attach the epidermis to the dermal extracellular matrix. Two disorders are caused by dysfunction of collagen VII, both characterized by skin and mucosa fragility, epidermolysis bullosa acquisita (EBA) a...

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Detalles Bibliográficos
Autores principales:	Schauer, Franziska, Nyström, Alexander, Kunz, Manfred, Hübner, Stefanie, Scholl, Sarah, Athanasiou, Ioannis, Alter, Svenja, Fischer, Judith, Has, Cristina, Kiritsi, Dimitra
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Frontiers Media S.A. 2022
Materias:	Immunology
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9021387/ https://www.ncbi.nlm.nih.gov/pubmed/35464429 http://dx.doi.org/10.3389/fimmu.2022.883967

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