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Multiple Intramyocardial Masses in an Otherwise Healthy 35-Year-Old Woman

Sarcoidosis with manifest cardiac involvement typically presents with heart failure, conduction abnormalities, or ventricular arrhythmias. Here, we present a case of a young woman whose presentation raised suspicion for metastatic cardiac disease of unknown primary origin. Further investigation reve...

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Detalles Bibliográficos
Autores principales: Powell, Ramsey G.G., Paulin, Frédéric L., Flemming, Jeffrey, Harris, Scott, Duffett, Stephen A.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9039576/
https://www.ncbi.nlm.nih.gov/pubmed/35495854
http://dx.doi.org/10.1016/j.cjco.2021.12.009
Descripción
Sumario:Sarcoidosis with manifest cardiac involvement typically presents with heart failure, conduction abnormalities, or ventricular arrhythmias. Here, we present a case of a young woman whose presentation raised suspicion for metastatic cardiac disease of unknown primary origin. Further investigation revealed cardiac sarcoidosis with multiple intramyocardial granulomatous masses in the absence of significant enlargement of hilar or mediastinal nodes. This case highlights the following: (i) sarcoidosis can mimic metastatic cardiac tumours; and (ii) hilar and mediastinal lymph nodes can be metabolically active in cardiac sarcoidosis in the absence of significant enlargement.