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Severe diabetic ketoacidosis and autoimmune pancreatitis with SIRS in an adolescent with LRBA deficiency – A rare complication of a common primary immunodeficiency disease

Common variable immunodeficiency is the most common primary immunodeficiency disorder. Lipopolysaccharide (LPS)-responsive beige-like anchor protein (LRBA) deficiency is categorized as a common variable immunodeficiency associated with autoimmune manifestations and inflammatory bowel diseases. We re...

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Detalles Bibliográficos
Autores principales:	Ravindran, Divya, Mugunthan, Rajavel Sagul Ramanuja, Shruthi, Tarikere Krishnamurthy, Jayaraman, Dhaarani
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Wolters Kluwer - Medknow 2022
Materias:	Case Report
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9067192/ https://www.ncbi.nlm.nih.gov/pubmed/35516664 http://dx.doi.org/10.4103/jfmpc.jfmpc_1220_21

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