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Multimodality Approach to a Complex Scimitar Syndrome: How Advanced Diagnostics Can Guide Therapeutic Strategies

We report an unusual association of scimitar syndrome with right diaphragmatic hernia, left-sided aortic arch with "aberrant right subclavian artery” in a 2-year-old boy who underwent stepwise transcatheter occlusion of a significant aortopulmonary collateral followed by surgical treatment for...

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Autores principales: Clemente, Alberto, Viganò, Gaia, Festa, Luigi, Remoli, Ettore, Marrone, Chiara, Federici, Duccio, Pak, Vitali, Chiappino, Dante, Santoro, Giuseppe, Ait-Ali, Lamia
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9125519/
https://www.ncbi.nlm.nih.gov/pubmed/35615212
http://dx.doi.org/10.1016/j.jaccas.2022.03.027
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author Clemente, Alberto
Viganò, Gaia
Festa, Luigi
Remoli, Ettore
Marrone, Chiara
Federici, Duccio
Pak, Vitali
Chiappino, Dante
Santoro, Giuseppe
Ait-Ali, Lamia
author_facet Clemente, Alberto
Viganò, Gaia
Festa, Luigi
Remoli, Ettore
Marrone, Chiara
Federici, Duccio
Pak, Vitali
Chiappino, Dante
Santoro, Giuseppe
Ait-Ali, Lamia
author_sort Clemente, Alberto
collection PubMed
description We report an unusual association of scimitar syndrome with right diaphragmatic hernia, left-sided aortic arch with "aberrant right subclavian artery” in a 2-year-old boy who underwent stepwise transcatheter occlusion of a significant aortopulmonary collateral followed by surgical treatment for the repair of the diaphragmatic hernia and esophageal compression. (Level of Difficulty: Advanced.)
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spelling pubmed-91255192022-05-24 Multimodality Approach to a Complex Scimitar Syndrome: How Advanced Diagnostics Can Guide Therapeutic Strategies Clemente, Alberto Viganò, Gaia Festa, Luigi Remoli, Ettore Marrone, Chiara Federici, Duccio Pak, Vitali Chiappino, Dante Santoro, Giuseppe Ait-Ali, Lamia JACC Case Rep Case Report We report an unusual association of scimitar syndrome with right diaphragmatic hernia, left-sided aortic arch with "aberrant right subclavian artery” in a 2-year-old boy who underwent stepwise transcatheter occlusion of a significant aortopulmonary collateral followed by surgical treatment for the repair of the diaphragmatic hernia and esophageal compression. (Level of Difficulty: Advanced.) Elsevier 2022-05-18 /pmc/articles/PMC9125519/ /pubmed/35615212 http://dx.doi.org/10.1016/j.jaccas.2022.03.027 Text en © 2022 The Authors https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Case Report
Clemente, Alberto
Viganò, Gaia
Festa, Luigi
Remoli, Ettore
Marrone, Chiara
Federici, Duccio
Pak, Vitali
Chiappino, Dante
Santoro, Giuseppe
Ait-Ali, Lamia
Multimodality Approach to a Complex Scimitar Syndrome: How Advanced Diagnostics Can Guide Therapeutic Strategies
title Multimodality Approach to a Complex Scimitar Syndrome: How Advanced Diagnostics Can Guide Therapeutic Strategies
title_full Multimodality Approach to a Complex Scimitar Syndrome: How Advanced Diagnostics Can Guide Therapeutic Strategies
title_fullStr Multimodality Approach to a Complex Scimitar Syndrome: How Advanced Diagnostics Can Guide Therapeutic Strategies
title_full_unstemmed Multimodality Approach to a Complex Scimitar Syndrome: How Advanced Diagnostics Can Guide Therapeutic Strategies
title_short Multimodality Approach to a Complex Scimitar Syndrome: How Advanced Diagnostics Can Guide Therapeutic Strategies
title_sort multimodality approach to a complex scimitar syndrome: how advanced diagnostics can guide therapeutic strategies
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9125519/
https://www.ncbi.nlm.nih.gov/pubmed/35615212
http://dx.doi.org/10.1016/j.jaccas.2022.03.027
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