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Incidental alpha-1-antitrypsin deficiency found in post-transplant liver allografts: Report of two cases
Alpha-1 antitrypsin deficiency is an autosomal recessive disease most commonly caused by misfolding of the Alpha-1-antitrypsin protein, which prevents its release from hepatocytes into the systemic circulation. This results in increased lifetime risk of liver and lung disease. Due to its variable pe...
Autores principales: | , , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Kare Publishing
2021
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9138925/ https://www.ncbi.nlm.nih.gov/pubmed/35782889 http://dx.doi.org/10.14744/hf.2020.2020.0013 |
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author | Lee, Jonathan Yoshida, Eric M. Mattman, Andre Marquez, Vladimir Bukhari, Hussam Farnell, David Yang, Hui-Min |
author_facet | Lee, Jonathan Yoshida, Eric M. Mattman, Andre Marquez, Vladimir Bukhari, Hussam Farnell, David Yang, Hui-Min |
author_sort | Lee, Jonathan |
collection | PubMed |
description | Alpha-1 antitrypsin deficiency is an autosomal recessive disease most commonly caused by misfolding of the Alpha-1-antitrypsin protein, which prevents its release from hepatocytes into the systemic circulation. This results in increased lifetime risk of liver and lung disease. Due to its variable penetrance, presentation and natural history, patients with alpha-1 antitrypsin deficiency are often underdiagnosed. In this report, we present two cases of alpha-1 antitrypsin deficiency in deceased-donor liver transplant allografts diagnosed post-transplant. There is currently no known adverse outcome directly linked to alpha-1 antitrypsin deficiency in the immediate post-transplant follow-up period. Thus, these allografts should not be excluded from transplantation. |
format | Online Article Text |
id | pubmed-9138925 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2021 |
publisher | Kare Publishing |
record_format | MEDLINE/PubMed |
spelling | pubmed-91389252022-07-01 Incidental alpha-1-antitrypsin deficiency found in post-transplant liver allografts: Report of two cases Lee, Jonathan Yoshida, Eric M. Mattman, Andre Marquez, Vladimir Bukhari, Hussam Farnell, David Yang, Hui-Min Hepatol Forum Case Report - Alpha-1-antitrypsin deficiency in liver allografts Alpha-1 antitrypsin deficiency is an autosomal recessive disease most commonly caused by misfolding of the Alpha-1-antitrypsin protein, which prevents its release from hepatocytes into the systemic circulation. This results in increased lifetime risk of liver and lung disease. Due to its variable penetrance, presentation and natural history, patients with alpha-1 antitrypsin deficiency are often underdiagnosed. In this report, we present two cases of alpha-1 antitrypsin deficiency in deceased-donor liver transplant allografts diagnosed post-transplant. There is currently no known adverse outcome directly linked to alpha-1 antitrypsin deficiency in the immediate post-transplant follow-up period. Thus, these allografts should not be excluded from transplantation. Kare Publishing 2021-01-08 /pmc/articles/PMC9138925/ /pubmed/35782889 http://dx.doi.org/10.14744/hf.2020.2020.0013 Text en © Copyright 2021 by Hepatology Forum - Available online at www.hepatologyforum.org https://creativecommons.org/licenses/by-nc/4.0/This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License. |
spellingShingle | Case Report - Alpha-1-antitrypsin deficiency in liver allografts Lee, Jonathan Yoshida, Eric M. Mattman, Andre Marquez, Vladimir Bukhari, Hussam Farnell, David Yang, Hui-Min Incidental alpha-1-antitrypsin deficiency found in post-transplant liver allografts: Report of two cases |
title | Incidental alpha-1-antitrypsin deficiency found in post-transplant liver allografts: Report of two cases |
title_full | Incidental alpha-1-antitrypsin deficiency found in post-transplant liver allografts: Report of two cases |
title_fullStr | Incidental alpha-1-antitrypsin deficiency found in post-transplant liver allografts: Report of two cases |
title_full_unstemmed | Incidental alpha-1-antitrypsin deficiency found in post-transplant liver allografts: Report of two cases |
title_short | Incidental alpha-1-antitrypsin deficiency found in post-transplant liver allografts: Report of two cases |
title_sort | incidental alpha-1-antitrypsin deficiency found in post-transplant liver allografts: report of two cases |
topic | Case Report - Alpha-1-antitrypsin deficiency in liver allografts |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9138925/ https://www.ncbi.nlm.nih.gov/pubmed/35782889 http://dx.doi.org/10.14744/hf.2020.2020.0013 |
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