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Ileal Bile Acid Transporter Inhibition Reduces Post-Transplant Diarrhea and Growth Failure in FIC1 Disease—A Case Report

Familial intrahepatic cholestasis 1 (FIC1) disease is a genetic disorder characterized by hepatic and gastrointestinal disease due to ATP8B1 deficiency, often requiring liver transplantation (LT). Extrahepatic symptoms, such as diarrhea, malabsorption, and failure to thrive, do not improve and inste...

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Detalles Bibliográficos
Autores principales:	Ohlendorf, Johanna, Goldschmidt, Imeke, Junge, Norman, Laue, Tobias, Nasser, Hamoud, Jäckel, Elmar, Mutschler, Frauke, Pfister, Eva-Doreen, Herebian, Diran, Keitel, Verena, Baumann, Ulrich
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2022
Materias:	Case Report
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9139332/ https://www.ncbi.nlm.nih.gov/pubmed/35626847 http://dx.doi.org/10.3390/children9050669

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