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Cor Triatriatum Dexter: Contrast Echocardiography Is Key to the Diagnosis of a Rare but Treatable Cause of Neonatal Persistent Cyanosis
Cor triatriatum dexter (CTD) is an extremely uncommon and underreported congenital cardiac anomaly in which the persistence of the embryonic right venous valve separates the right atrium into two chambers with varying degrees of obstruction to antegrade flow and variable degree of right to left shun...
Autores principales: | , , , , , , , , , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2022
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9139359/ https://www.ncbi.nlm.nih.gov/pubmed/35626853 http://dx.doi.org/10.3390/children9050676 |
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author | Picciolli, Irene Francescato, Gaia Colli, Anna Maria Cappelleri, Alessia Mayer, Alessandra Raschetti, Roberto Di Cosola, Roberta Pisaniello, Marco Annoni, Giuseppe Alberto Papa, Marco Maldi, Mimoza Olivieri, Guido Mosca, Fabio Marianeschi, Stefano |
author_facet | Picciolli, Irene Francescato, Gaia Colli, Anna Maria Cappelleri, Alessia Mayer, Alessandra Raschetti, Roberto Di Cosola, Roberta Pisaniello, Marco Annoni, Giuseppe Alberto Papa, Marco Maldi, Mimoza Olivieri, Guido Mosca, Fabio Marianeschi, Stefano |
author_sort | Picciolli, Irene |
collection | PubMed |
description | Cor triatriatum dexter (CTD) is an extremely uncommon and underreported congenital cardiac anomaly in which the persistence of the embryonic right venous valve separates the right atrium into two chambers with varying degrees of obstruction to antegrade flow and variable degree of right to left shunt at atrial level. Depending on the size of the valves, clinical manifestations vary from absence of symptoms to severe hypoxia, requiring urgent surgical correction. We herein describe the diagnostic difficulties in a case of neonatal CTD, who developed increasingly severe and unresponsive cyanosis, first interpreted as postnatal maladjustment with pulmonary hypertension. The failure to respond to oxygen and pulmonary vasodilators led us to reconsider a different diagnosis. The use of contrast echocardiography improved the diagnostic performance of transthoracic echocardiogram (TTE) and revealed a massive right-to-left shunt secondary to the presence of an atrial membrane that required urgent surgery. |
format | Online Article Text |
id | pubmed-9139359 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2022 |
publisher | MDPI |
record_format | MEDLINE/PubMed |
spelling | pubmed-91393592022-05-28 Cor Triatriatum Dexter: Contrast Echocardiography Is Key to the Diagnosis of a Rare but Treatable Cause of Neonatal Persistent Cyanosis Picciolli, Irene Francescato, Gaia Colli, Anna Maria Cappelleri, Alessia Mayer, Alessandra Raschetti, Roberto Di Cosola, Roberta Pisaniello, Marco Annoni, Giuseppe Alberto Papa, Marco Maldi, Mimoza Olivieri, Guido Mosca, Fabio Marianeschi, Stefano Children (Basel) Case Report Cor triatriatum dexter (CTD) is an extremely uncommon and underreported congenital cardiac anomaly in which the persistence of the embryonic right venous valve separates the right atrium into two chambers with varying degrees of obstruction to antegrade flow and variable degree of right to left shunt at atrial level. Depending on the size of the valves, clinical manifestations vary from absence of symptoms to severe hypoxia, requiring urgent surgical correction. We herein describe the diagnostic difficulties in a case of neonatal CTD, who developed increasingly severe and unresponsive cyanosis, first interpreted as postnatal maladjustment with pulmonary hypertension. The failure to respond to oxygen and pulmonary vasodilators led us to reconsider a different diagnosis. The use of contrast echocardiography improved the diagnostic performance of transthoracic echocardiogram (TTE) and revealed a massive right-to-left shunt secondary to the presence of an atrial membrane that required urgent surgery. MDPI 2022-05-06 /pmc/articles/PMC9139359/ /pubmed/35626853 http://dx.doi.org/10.3390/children9050676 Text en © 2022 by the authors. https://creativecommons.org/licenses/by/4.0/Licensee MDPI, Basel, Switzerland. This article is an open access article distributed under the terms and conditions of the Creative Commons Attribution (CC BY) license (https://creativecommons.org/licenses/by/4.0/). |
spellingShingle | Case Report Picciolli, Irene Francescato, Gaia Colli, Anna Maria Cappelleri, Alessia Mayer, Alessandra Raschetti, Roberto Di Cosola, Roberta Pisaniello, Marco Annoni, Giuseppe Alberto Papa, Marco Maldi, Mimoza Olivieri, Guido Mosca, Fabio Marianeschi, Stefano Cor Triatriatum Dexter: Contrast Echocardiography Is Key to the Diagnosis of a Rare but Treatable Cause of Neonatal Persistent Cyanosis |
title | Cor Triatriatum Dexter: Contrast Echocardiography Is Key to the Diagnosis of a Rare but Treatable Cause of Neonatal Persistent Cyanosis |
title_full | Cor Triatriatum Dexter: Contrast Echocardiography Is Key to the Diagnosis of a Rare but Treatable Cause of Neonatal Persistent Cyanosis |
title_fullStr | Cor Triatriatum Dexter: Contrast Echocardiography Is Key to the Diagnosis of a Rare but Treatable Cause of Neonatal Persistent Cyanosis |
title_full_unstemmed | Cor Triatriatum Dexter: Contrast Echocardiography Is Key to the Diagnosis of a Rare but Treatable Cause of Neonatal Persistent Cyanosis |
title_short | Cor Triatriatum Dexter: Contrast Echocardiography Is Key to the Diagnosis of a Rare but Treatable Cause of Neonatal Persistent Cyanosis |
title_sort | cor triatriatum dexter: contrast echocardiography is key to the diagnosis of a rare but treatable cause of neonatal persistent cyanosis |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9139359/ https://www.ncbi.nlm.nih.gov/pubmed/35626853 http://dx.doi.org/10.3390/children9050676 |
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