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Treatment with IFB-088 Improves Neuropathy in CMT1A and CMT1B Mice
Charcot-Marie-Tooth disease type 1A (CMT1A), caused by duplication of the peripheral myelin protein 22 (PMP22) gene, and CMT1B, caused by mutations in myelin protein zero (MPZ) gene, are the two most common forms of demyelinating CMT (CMT1), and no treatments are available for either. Prior studies...
Autores principales: | Bai, Yunhong, Treins, Caroline, Volpi, Vera G., Scapin, Cristina, Ferri, Cinzia, Mastrangelo, Rosa, Touvier, Thierry, Florio, Francesca, Bianchi, Francesca, Del Carro, Ubaldo, Baas, Frank F., Wang, David, Miniou, Pierre, Guedat, Philippe, Shy, Michael E., D’Antonio, Maurizio |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Springer US
2022
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9167212/ https://www.ncbi.nlm.nih.gov/pubmed/35501630 http://dx.doi.org/10.1007/s12035-022-02838-y |
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