Cargando…

Assessing thrombogenesis and treatment response in congenital thrombotic thrombocytopenic purpura

Despite clinical remission and normal platelet counts, congenital TTP (cTTP) is associated with non‐overt symptoms. Prophylactic ADAMTS13 replacement therapy such as plasma infusion (PI) prevents acute episodes and improves symptomatology. There is no current method to investigate disease severity o...

Descripción completa

Detalles Bibliográficos
Autores principales:	Alwan, Ferras, Vendramin, Chiara, Budde, Ulrich, Liesner, Ri, Taylor, Alice, Thomas, Mari, Lämmle, Bernhard, Scully, Marie
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	John Wiley and Sons Inc. 2021
Materias:	Sickle Cell, Thrombosis, and Haematology
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9175835/ https://www.ncbi.nlm.nih.gov/pubmed/35845267 http://dx.doi.org/10.1002/jha2.178

Ejemplares similares

Unmet needs in the management of immune‐mediated thrombotic thrombocytopenic purpura and the potential role of caplacizumab in the UK—A modified‐Delphi study
por: Scully, Marie, et al.
Publicado: (2022)

Plasma exchange for COVID‐19 thrombo‐inflammatory disease
por: Arulkumaran, Nishkantha, et al.
Publicado: (2020)

Bleeding outcomes in thrombocytopenic acute leukemic patients with venous thromboembolism
por: Wilson, Nathaniel R., et al.
Publicado: (2020)

Thrombotic microangiopathies: First report of 294 cases from a single institution experience in Argentina
por: Dos Santos, Célia, et al.
Publicado: (2021)

Acute dilated cardiomyopathy in the setting of catastrophic antiphospholipid syndrome and thrombotic microangiopathy: A case series and review
por: Hermel, Melody, et al.
Publicado: (2020)

Alterations in B- and circulating T-follicular helper cell subsets in immune thrombotic thrombocytopenic purpura
por: Shin, Jin-Sup, et al.
Publicado: (2022)

Complement and cytokine response in acute Thrombotic Thrombocytopenic Purpura
por: Westwood, John-Paul, et al.
Publicado: (2014)

Efficacy and safety of open‐label caplacizumab in patients with exacerbations of acquired thrombotic thrombocytopenic purpura in the HERCULES study
por: Knoebl, Paul, et al.
Publicado: (2019)

Is sickle cell disease a risk factor for severe COVID‐19 outcomes in hospitalized patients? A multicenter national retrospective cohort study
por: Abdulrahman, Abdulkarim, et al.
Publicado: (2021)

Clusters of pain trajectories among patients with sickle cell disease hospitalized for vaso‐occlusive crisis: A data‐driven approach
por: Rodday, Angie Mae, et al.
Publicado: (2020)

Patterns of healthcare utilization among patients with sickle cell disease hospitalized with pain crises
por: Rodday, Angie Mae, et al.
Publicado: (2020)

Mild anemia as a single independent predictor of mortality in patients with COVID‐19
por: Tremblay, Douglas, et al.
Publicado: (2021)

In‐hospital mortality in SARS‐CoV‐2 stratified by hemoglobin levels: A retrospective study
por: Al‐Jarallah, Mohammed, et al.
Publicado: (2021)

Blood group type A secretors are associated with a higher risk of COVID‐19 cardiovascular disease complications
por: Mankelow, Tosti J., et al.
Publicado: (2021)

The effect of underlying inflammation on iron metabolism, cardiovascular risk and renal function in patients with type 2 diabetes
por: Ndevahoma, Fransina, et al.
Publicado: (2021)

The net benefit of thrombolysis in the management of intermediate risk pulmonary embolism: Systematic review and meta‐analysis
por: Alcedo, Pedro E., et al.
Publicado: (2020)

Age‐specific differences in the magnitude of malaria‐related anemia during low and high malaria seasons in rural Zambian children
por: Acheampong, Clement O., et al.
Publicado: (2021)

A pilot clinical phase II trial MemSID: Acute and durable changes of red blood cells of sickle cell disease patients on memantine treatment
por: Mahkro, Asya, et al.
Publicado: (2020)

Alpha‐globin gene triplication and its effect in beta‐thalassemia carrier, sickle cell trait, and healthy individual
por: Hamid, Mohammad, et al.
Publicado: (2021)

A novel cause of DKC1‐related bone marrow failure: Partial deletion of the 3′ untranslated region
por: Arthur, Jonathan W., et al.
Publicado: (2021)

Von Willebrand disease type Vicenza: In search of a classification for the archetype of reduced von Willebrand factor survival
por: Casonato, Alessandra, et al.
Publicado: (2021)

A retrospective analysis of venous thromboembolism trends in chemotherapy‐induced anemia: Red blood cell transfusion versus erythrocyte stimulating agent administration
por: Bryer, Emily J., et al.
Publicado: (2020)

Gabapentin for acute pain in sickle cell disease: A randomized double‐blinded placebo‐controlled phase II clinical trial
por: Puri, Latika, et al.
Publicado: (2021)

Unsupervised machine learning algorithms identify expected haemorrhage relationships but define unexplained coagulation profiles mapping to thrombotic phenotypes in hereditary haemorrhagic telangiectasia
por: Mukhtar, Ghazel, et al.
Publicado: (2023)

A novel von Willebrand factor multimer ratio as marker of disease activity in thrombotic thrombocytopenic purpura
por: Falter, Tanja, et al.
Publicado: (2023)

Morbidities and mortality in patients with hereditary thrombotic thrombocytopenic purpura
por: Borogovac, Azra, et al.
Publicado: (2022)

A third form of thrombotic thrombocytopenic purpura?
por: Lämmle, Bernhard
Publicado: (2022)

Thrombotic Thrombocytopenic Purpura: Pathophysiology, Diagnosis, and Management
por: Sukumar, Senthil, et al.
Publicado: (2021)

Altered type 1 interferon responses in alloimmunized and nonalloimmunized patients with sickle cell disease
por: Madany, Emaan, et al.
Publicado: (2021)

Erytra blood group analyser and kode technology testing of SARS‐CoV‐2 antibodies among convalescent patients and vaccinated individuals
por: Weinstock, Christof, et al.
Publicado: (2021)

Paroxysmal nocturnal haemoglobinuria, diagnosis and haematological findings, first report from Iran, model for developing countries
por: Jahangirpour, Mohammadali, et al.
Publicado: (2022)

Resource utilization and treatment costs of patients with severe hemophilia A: Real‐world data from the ATHNdataset
por: Recht, Michael, et al.
Publicado: (2022)

Facilitating EMA binding test performance using fluorescent beads combined with next‐generation sequencing
por: Glenthøj, Andreas, et al.
Publicado: (2021)

Degradation of red blood cell deformability during cold storage in blood bags
por: Islamzada, Emel, et al.
Publicado: (2021)

Impact of aspirin on bleeding and blood product usage in off‐pump and on‐pump coronary artery bypass graft surgery
por: Little, Christopher, et al.
Publicado: (2022)

Cytopenia associated with copper deficiency
por: Uchino, Kaori, et al.
Publicado: (2021)

Comparison of inhibitory effects of irreversible and reversible Btk inhibitors on platelet function
por: Tullemans, Bibian M.E., et al.
Publicado: (2021)

A practical and effective strategy in East Asia to prevent anti‐D alloimmunization in patients by C/c phenotyping of serologic RhD‐negative blood donors
por: Ito, Shoichi, et al.
Publicado: (2021)

Homozygous sickle cell disease related mortality in Senegal (2011–2020)
por: Seck, Moussa, et al.
Publicado: (2021)

Routine management, healthcare resource use and patient and carer‐reported outcomes of patients with transfusion‐dependent β‐thalassaemia in the United Kingdom: A mixed methods observational study
por: Shah, Farrukh, et al.
Publicado: (2021)

Cannot write session to /tmp/vufind_sessions/sess_v8u573t6k4tiv5cnbs0cmj52ta