Diagnostic dilemma in diagnosing rare cause of protein losing enteropathy: Waldmann's disease

Waldmann's disease, or primary intestinal lymphangiectasia, is an unusual cause of protein‐losing enteropathy primarily characterized by lymphopenia, hypoalbuminemia, and hypogammaglobulinemia. However, variable clinical presentations result dilemmas in diagnosis and effective management. We pr...

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Detalles Bibliográficos
Autores principales: Prajapati, Sarita, Bohara, Sujan, Mainali, Gaurab, Karki, Samikshya, Thapa, Sharan, Aryal, Nirjala
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2022
Materias:
Case Reports
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9211774/
https://www.ncbi.nlm.nih.gov/pubmed/35769238
http://dx.doi.org/10.1002/ccr3.5992
Descripción
Sumario:Waldmann's disease, or primary intestinal lymphangiectasia, is an unusual cause of protein‐losing enteropathy primarily characterized by lymphopenia, hypoalbuminemia, and hypogammaglobulinemia. However, variable clinical presentations result dilemmas in diagnosis and effective management. We present a toddler diagnosed with Waldmann's disease managed with a high‐protein diet and medium‐chain triglyceride supplementation.

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