Assessment of Respiratory Function and Need for Noninvasive Ventilation in a Cohort of Patients with Myotonic Dystrophy Type 1 Followed at One Single Expert Center

INTRODUCTION: Respiratory insufficiency is one of the main causes of death in myotonic dystrophy type 1 (DM1). Although there is general consensus that these patients have a restrictive ventilatory pattern, hypoventilation, chronic hypercapnia, and sleep disturbances, the prevalence of respiratory d...

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Detalles Bibliográficos
Autores principales: Ferrari Aggradi, Carola R., Falcier, Elisa, Lizio, Andrea, Pirola, Alice, Casiraghi, Jacopo, Zanolini, Alice, Carraro, Elena, Mauro, Luca, Rao, Fabrizio, Roma, Elisabetta, Iannello, Antonino, De Mattia, Elisa, Barp, Andrea, Lupone, Sara, Gatti, Valentina, Italiano, Cristina, Sansone, Valeria A.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi 2022
Materias:
Research Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9233572/
https://www.ncbi.nlm.nih.gov/pubmed/35762008
http://dx.doi.org/10.1155/2022/2321909

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