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Case Report: Tocilizumab Treatment for VEXAS Syndrome With Relapsing Polychondritis: A Single-Center, 1-Year Longitudinal Observational Study In Japan

Vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic (VEXAS) syndrome is an autoinflammatory disease caused by somatic variants in the UBA1 gene that lead to severe systemic inflammation and myelodysplastic syndrome. Although no standard therapy has been established yet, azacitidine and bone mar...

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Detalles Bibliográficos
Autores principales:	Kunishita, Yosuke, Kirino, Yohei, Tsuchida, Naomi, Maeda, Ayaka, Sato, Yuichiro, Takase-Minegishi, Kaoru, Yoshimi, Ryusuke, Nakajima, Hideaki
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Frontiers Media S.A. 2022
Materias:	Immunology
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9234115/ https://www.ncbi.nlm.nih.gov/pubmed/35769485 http://dx.doi.org/10.3389/fimmu.2022.901063

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