Cargando…

Case Report: Tocilizumab Treatment for VEXAS Syndrome With Relapsing Polychondritis: A Single-Center, 1-Year Longitudinal Observational Study In Japan

Vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic (VEXAS) syndrome is an autoinflammatory disease caused by somatic variants in the UBA1 gene that lead to severe systemic inflammation and myelodysplastic syndrome. Although no standard therapy has been established yet, azacitidine and bone mar...

Descripción completa

Detalles Bibliográficos
Autores principales:	Kunishita, Yosuke, Kirino, Yohei, Tsuchida, Naomi, Maeda, Ayaka, Sato, Yuichiro, Takase-Minegishi, Kaoru, Yoshimi, Ryusuke, Nakajima, Hideaki
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Frontiers Media S.A. 2022
Materias:	Immunology
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9234115/ https://www.ncbi.nlm.nih.gov/pubmed/35769485 http://dx.doi.org/10.3389/fimmu.2022.901063

Ejemplares similares

Risk of Macrophage Activation Syndrome in Patients with Adult-Onset Still’s Disease Treated with IL-1 and IL-6 Inhibitors: A Meta-analysis and Single-Center Experience
por: Adachi, Soichiro, et al.
Publicado: (2023)

Incidence and Distinct Features of Immune Checkpoint Inhibitor-Related Myositis From Idiopathic Inflammatory Myositis: A Single-Center Experience With Systematic Literature Review and Meta-Analysis
por: Hamada, Naoki, et al.
Publicado: (2021)

Dysregulated heme oxygenase-1(low) M2-like macrophages augment lupus nephritis via Bach1 induced by type I interferons
por: Kishimoto, Daiga, et al.
Publicado: (2018)

The Roles of Monocytes and Macrophages in Behçet’s Disease With Focus on M1 and M2 Polarization
por: Hirahara, Lisa, et al.
Publicado: (2022)

Comparison between idiopathic and VEXAS-relapsing polychondritis: analysis of a French case series of 95 patients
por: Khitri, Mohamed-Yacine, et al.
Publicado: (2022)

Incidence and Risk of Hematological Adverse Events Associated With Immune Checkpoint Inhibitors: A Systematic Literature Review and Meta-Analysis
por: Ohashi, Takuma, et al.
Publicado: (2023)

The predictive prognostic factors for polymyositis/dermatomyositis-associated interstitial lung disease
por: Sugiyama, Yumiko, et al.
Publicado: (2018)

Case Report: Coexistence of Multiple Myeloma and Auricular Chondritis in VEXAS Syndrome
por: Matsumoto, Haruki, et al.
Publicado: (2022)

TRIM21 Dysfunction Enhances Aberrant B-Cell Differentiation in Autoimmune Pathogenesis
por: Kunishita, Yosuke, et al.
Publicado: (2020)

Protective effect of hydroxychloroquine on infections in patients with systemic lupus erythematosus: an observational study using the LUNA registry
por: Hidekawa, Chiharu, et al.
Publicado: (2023)

Ocular Involvement in Relapsing Polychondritis
por: Fukuda, Ken, et al.
Publicado: (2021)

Continuous evolution of clinical phenotype in 578 Japanese patients with Behçet’s disease: a retrospective observational study
por: Kirino, Yohei, et al.
Publicado: (2016)

Relapsing Polychondritis
por: Sosada, Beata, et al.
Publicado: (2014)

Relapsing Polychondritis
por: Sarangapani, Arulprakash, et al.
Publicado: (2016)

Relapsing Polychondritis
por: Taniyama, Daisuke, et al.
Publicado: (2019)

The PRY/SPRY domain of pyrin/TRIM20 interacts with β(2)-microglobulin to promote inflammasome formation
por: Samukawa, Sei, et al.
Publicado: (2021)

Lung Cancer Complicated by Relapsing Polychondritis
por: Arakawa, Sosuke, et al.
Publicado: (2022)

Anti-interferon-γ Antibody-seropositive Disseminated Nontuberculous Mycobacterial Infection Mimicking POEMS and TAFRO Syndromes
por: Hidekawa, Chiharu, et al.
Publicado: (2022)

Relapsing Polychondritis and Ulcerative Colitis
por: Almadi, Majid A., et al.
Publicado: (2010)

Prevalence and comorbidity of relapsing polychondritis
por: Ludvigsson, Jonas F, et al.
Publicado: (2016)

Relapsing polychondritis and otologic findings
por: Derin, Serhan, et al.
Publicado: (2014)

Severe panuveitis with relapsing polychondritis
por: Masuda, Naonori, et al.
Publicado: (2018)

Relapsing Polychondritis: An Updated Review
por: Borgia, Francesco, et al.
Publicado: (2018)

Relapsing Polychondritis and Aseptic Meningoencephalitis
por: Yokota, Kazuhiro, et al.
Publicado: (2022)

Exacerbation of Ulcerative Colitis with Tocilizumab: A Report of Two Cases, One with Takayasu Arteritis and the Other with Relapsing Polychondritis
por: Hanioka, Yusuke, et al.
Publicado: (2020)

Co-occurrence of relapsing polychondritis and autoimmune thyroid diseases
por: Nakajima, Toshiki, et al.
Publicado: (2022)

Relapsing polychondritis detected in PET/CT
por: Czepczyński, Rafał, et al.
Publicado: (2012)

Relapsing Polychondritis Following Alopecia Areata
por: Starr, John C., et al.
Publicado: (2010)

Relapsing polychondritis presenting with inflammatory pseudotumor
por: Eun, Yeong Hee, et al.
Publicado: (2016)

Refractory relapsing polychondritis: challenges and solutions
por: Lekpa, Fernando Kemta, et al.
Publicado: (2018)

Relapsing polychondritis – analysis of symptoms and criteria
por: Maciążek-Chyra, Beata, et al.
Publicado: (2019)

Relapsing polychondritis with large airway involvement
por: Yu, Christiaan, et al.
Publicado: (2019)

Early Recognition and Treatment of Relapsing Polychondritis
por: Yanagihara, Toyoshi, et al.
Publicado: (2022)

Risk factors for the recurrence of relapsing polychondritis
por: Yoshida, Tsuneyasu, et al.
Publicado: (2022)

Relapsing polychondritis: focus on cardiac involvement
por: Yin, Ruxue, et al.
Publicado: (2023)

VEXAS syndrome
por: Grayson, Peter C., et al.
Publicado: (2021)

VEXAS-Syndrom
por: Zeeck, M., et al.
Publicado: (2022)

Clinical and Genetic Aspects of Behçet's Disease in Japan
por: Kirino, Yohei, et al.
Publicado: (2019)

Keratouveitis as a First Presentation of Relapsing Polychondritis
por: Sallam, Ahmed, et al.
Publicado: (2010)

The obstructive siblings: Relapsing polychondritis without chondritis?
por: Sæverud, Haavard A., et al.
Publicado: (2013)

Cannot write session to /tmp/vufind_sessions/sess_cql9k5qa6t07i07pcog9qqhc6m