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Diagnosing Pediatric Patients With Hereditary C1-Inhibitor Deficiency—Experience From the Hungarian Angioedema Center of Reference and Excellence

BACKGROUND: Hereditary Angioedema with C1-inhibitor deficiency (C1-INH-HAE) is a rare disease characterized by recurrent subcutaneous and/or submucosal edematous (HAE) episodes, which may occur at any age. The mean age of the symptom onset is 10–12 years. Diagnostic protocols differ by age group and...

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Detalles Bibliográficos
Autores principales:	Andrási, Noémi, Balla, Zsuzsanna, Visy, Beáta, Szilágyi, Ágnes, Csuka, Dorottya, Varga, Lilian, Farkas, Henriette
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Frontiers Media S.A. 2022
Materias:	Allergy
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9234934/ https://www.ncbi.nlm.nih.gov/pubmed/35769571 http://dx.doi.org/10.3389/falgy.2022.860355

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