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Precapillary pulmonary arterial hypertension in a patient with Proteus syndrome

Proteus syndrome is a rare progressive multisystem disorder characterized by asymmetric, disproportionate overgrowth of bone, skin, and other tissue types. Molecular pathogenesis has been identified as somatic activating mutations of the AKT1 gene. The presentation of Proteus syndrome is exceptional...

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Detalles Bibliográficos
Autores principales:	Mathavan, Akash, Mathavan, Akshay, Vahdatpour, Cyrus, Eagan, Christina, Kalra, Saminder Singh, Ataya, Ali
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	John Wiley and Sons Inc. 2022
Materias:	Case Reports
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9235868/ https://www.ncbi.nlm.nih.gov/pubmed/35783033 http://dx.doi.org/10.1002/pul2.12098

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