Case Report: Primary Thoracic Low-Grade Fibromyxoid Sarcoma in a Young Girl Presenting With Mediastinal Mass Syndrome

Low-grade fibromyxoid sarcomas (LGFMSs) are typically adult-onset tumors that arise from the extremities. Here, we report an exceptional case of primary thoracic LGFMS in an 8-year-old girl that resulted in mediastinal syndrome. In reporting this case, we discuss the clinical challenges, role of mol...

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Autores principales: Chan, Yat Chi, Kan, Amanda N. C., Yuen, Liz Y. P., Wan, Innes Y. P., Fung, Kevin K. F., Cheung, Yiu-fai, Leung, Karen K. Y., Ku, Dennis T. L., Liu, Anthony P. Y.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2022
Materias:
Pediatrics
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9247646/
https://www.ncbi.nlm.nih.gov/pubmed/35783305
http://dx.doi.org/10.3389/fped.2022.885068
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author Chan, Yat Chi
Kan, Amanda N. C.
Yuen, Liz Y. P.
Wan, Innes Y. P.
Fung, Kevin K. F.
Cheung, Yiu-fai
Leung, Karen K. Y.
Ku, Dennis T. L.
Liu, Anthony P. Y.
author_facet Chan, Yat Chi
Kan, Amanda N. C.
Yuen, Liz Y. P.
Wan, Innes Y. P.
Fung, Kevin K. F.
Cheung, Yiu-fai
Leung, Karen K. Y.
Ku, Dennis T. L.
Liu, Anthony P. Y.
author_sort Chan, Yat Chi
collection PubMed
description Low-grade fibromyxoid sarcomas (LGFMSs) are typically adult-onset tumors that arise from the extremities. Here, we report an exceptional case of primary thoracic LGFMS in an 8-year-old girl that resulted in mediastinal syndrome. In reporting this case, we discuss the clinical challenges, role of molecular profiling and review reported cases of pediatric thoracic LGFMSs.
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spelling pubmed-92476462022-07-02 Case Report: Primary Thoracic Low-Grade Fibromyxoid Sarcoma in a Young Girl Presenting With Mediastinal Mass Syndrome Chan, Yat Chi Kan, Amanda N. C. Yuen, Liz Y. P. Wan, Innes Y. P. Fung, Kevin K. F. Cheung, Yiu-fai Leung, Karen K. Y. Ku, Dennis T. L. Liu, Anthony P. Y. Front Pediatr Pediatrics Low-grade fibromyxoid sarcomas (LGFMSs) are typically adult-onset tumors that arise from the extremities. Here, we report an exceptional case of primary thoracic LGFMS in an 8-year-old girl that resulted in mediastinal syndrome. In reporting this case, we discuss the clinical challenges, role of molecular profiling and review reported cases of pediatric thoracic LGFMSs. Frontiers Media S.A. 2022-06-17 /pmc/articles/PMC9247646/ /pubmed/35783305 http://dx.doi.org/10.3389/fped.2022.885068 Text en Copyright © 2022 Chan, Kan, Yuen, Wan, Fung, Cheung, Leung, Ku and Liu. https://creativecommons.org/licenses/by/4.0/This is an open-access article distributed under the terms of the Creative Commons Attribution License (CC BY). The use, distribution or reproduction in other forums is permitted, provided the original author(s) and the copyright owner(s) are credited and that the original publication in this journal is cited, in accordance with accepted academic practice. No use, distribution or reproduction is permitted which does not comply with these terms.
spellingShingle Pediatrics
Chan, Yat Chi
Kan, Amanda N. C.
Yuen, Liz Y. P.
Wan, Innes Y. P.
Fung, Kevin K. F.
Cheung, Yiu-fai
Leung, Karen K. Y.
Ku, Dennis T. L.
Liu, Anthony P. Y.
Case Report: Primary Thoracic Low-Grade Fibromyxoid Sarcoma in a Young Girl Presenting With Mediastinal Mass Syndrome
title Case Report: Primary Thoracic Low-Grade Fibromyxoid Sarcoma in a Young Girl Presenting With Mediastinal Mass Syndrome
title_full Case Report: Primary Thoracic Low-Grade Fibromyxoid Sarcoma in a Young Girl Presenting With Mediastinal Mass Syndrome
title_fullStr Case Report: Primary Thoracic Low-Grade Fibromyxoid Sarcoma in a Young Girl Presenting With Mediastinal Mass Syndrome
title_full_unstemmed Case Report: Primary Thoracic Low-Grade Fibromyxoid Sarcoma in a Young Girl Presenting With Mediastinal Mass Syndrome
title_short Case Report: Primary Thoracic Low-Grade Fibromyxoid Sarcoma in a Young Girl Presenting With Mediastinal Mass Syndrome
title_sort case report: primary thoracic low-grade fibromyxoid sarcoma in a young girl presenting with mediastinal mass syndrome
topic Pediatrics
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9247646/
https://www.ncbi.nlm.nih.gov/pubmed/35783305
http://dx.doi.org/10.3389/fped.2022.885068
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