Isolated Langerhans Cell Histiocytosis of the Vulva in a 28-Year-Old Lady: A Report of a Case and Brief Review of the Literature

Langerhans cell histiocytosis (LCH) is a rare, proliferative disorder of Langerhans' cells. The presentation can vary from single organ involvement to multisystem and disseminated in severe cases, affecting children more than adults. Isolated vulvar involvement of LCH in a 28-year-old woman has...

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Autores principales: Sadati, Maryam Sadat, Todarbary, Nafiseh, Sari Aslani, Fatemeh, Hadibarhaghtalab, Maryam
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi 2022
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9256389/
https://www.ncbi.nlm.nih.gov/pubmed/35801255
http://dx.doi.org/10.1155/2022/8483008
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author Sadati, Maryam Sadat
Todarbary, Nafiseh
Sari Aslani, Fatemeh
Hadibarhaghtalab, Maryam
author_facet Sadati, Maryam Sadat
Todarbary, Nafiseh
Sari Aslani, Fatemeh
Hadibarhaghtalab, Maryam
author_sort Sadati, Maryam Sadat
collection PubMed
description Langerhans cell histiocytosis (LCH) is a rare, proliferative disorder of Langerhans' cells. The presentation can vary from single organ involvement to multisystem and disseminated in severe cases, affecting children more than adults. Isolated vulvar involvement of LCH in a 28-year-old woman has rarely been described and also there are limited data for diagnosis and treatment. Herein, we report the case of a 28-year-old woman with isolated vulvar LCH, misdiagnosed with herpes simplex infection, successfully treated with thalidomide.
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spelling pubmed-92563892022-07-06 Isolated Langerhans Cell Histiocytosis of the Vulva in a 28-Year-Old Lady: A Report of a Case and Brief Review of the Literature Sadati, Maryam Sadat Todarbary, Nafiseh Sari Aslani, Fatemeh Hadibarhaghtalab, Maryam Case Rep Dermatol Med Case Report Langerhans cell histiocytosis (LCH) is a rare, proliferative disorder of Langerhans' cells. The presentation can vary from single organ involvement to multisystem and disseminated in severe cases, affecting children more than adults. Isolated vulvar involvement of LCH in a 28-year-old woman has rarely been described and also there are limited data for diagnosis and treatment. Herein, we report the case of a 28-year-old woman with isolated vulvar LCH, misdiagnosed with herpes simplex infection, successfully treated with thalidomide. Hindawi 2022-06-28 /pmc/articles/PMC9256389/ /pubmed/35801255 http://dx.doi.org/10.1155/2022/8483008 Text en Copyright © 2022 Maryam Sadat Sadati et al. https://creativecommons.org/licenses/by/4.0/This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Sadati, Maryam Sadat
Todarbary, Nafiseh
Sari Aslani, Fatemeh
Hadibarhaghtalab, Maryam
Isolated Langerhans Cell Histiocytosis of the Vulva in a 28-Year-Old Lady: A Report of a Case and Brief Review of the Literature
title Isolated Langerhans Cell Histiocytosis of the Vulva in a 28-Year-Old Lady: A Report of a Case and Brief Review of the Literature
title_full Isolated Langerhans Cell Histiocytosis of the Vulva in a 28-Year-Old Lady: A Report of a Case and Brief Review of the Literature
title_fullStr Isolated Langerhans Cell Histiocytosis of the Vulva in a 28-Year-Old Lady: A Report of a Case and Brief Review of the Literature
title_full_unstemmed Isolated Langerhans Cell Histiocytosis of the Vulva in a 28-Year-Old Lady: A Report of a Case and Brief Review of the Literature
title_short Isolated Langerhans Cell Histiocytosis of the Vulva in a 28-Year-Old Lady: A Report of a Case and Brief Review of the Literature
title_sort isolated langerhans cell histiocytosis of the vulva in a 28-year-old lady: a report of a case and brief review of the literature
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9256389/
https://www.ncbi.nlm.nih.gov/pubmed/35801255
http://dx.doi.org/10.1155/2022/8483008
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