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Pediatric Langerhans Cell Histiocytosis: An Aggressive Presentation

Encountering a young child with an enlarging painless facial swelling often raises concerns in the treating physician about the possibility of a congenital lesion or an unfavorable pediatric tumor. We discuss a case of a female child who presented with multiple craniofacial swellings, which turned o...

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Detalles Bibliográficos
Autores principales: Suthersan, Shasikala, Ong, Fei Ming, Maruthamuthu, Thevagi, Periasamy, Chenthilnathan, Goh, Bee-See
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9258628/
https://www.ncbi.nlm.nih.gov/pubmed/35812621
http://dx.doi.org/10.7759/cureus.25684
Descripción
Sumario:Encountering a young child with an enlarging painless facial swelling often raises concerns in the treating physician about the possibility of a congenital lesion or an unfavorable pediatric tumor. We discuss a case of a female child who presented with multiple craniofacial swellings, which turned out to be Langerhans cell histiocytosis (LCH). She was subsequently diagnosed with multisystem LCH (MS-LCH) with risk-organ involvement, which included the craniofacial bones, skin, hemopoietic system, and liver. We analyze the various presentations and systemic complications of this rare pediatric tumor, LCH, with an aim to address the diagnostic dilemma associated with this great masquerader.