The Exocrine Pancreas in Cystic Fibrosis in the Era of CFTR Modulation: A Mini Review
Cystic fibrosis (CF) is a common disorder of autosomal recessive inheritance, that once conferred a life expectancy of only a few months. Over recent years, significant advances have been made to CF therapeutic approaches, changing the face of the disease, and facilitating the partial restoration of...
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Formato: | Online Artículo Texto |
Lenguaje: | English |
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Frontiers Media S.A.
2022
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Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9271761/ https://www.ncbi.nlm.nih.gov/pubmed/35832587 http://dx.doi.org/10.3389/fped.2022.914790 |
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author | McKay, Isabelle R. Ooi, Chee Y. |
author_facet | McKay, Isabelle R. Ooi, Chee Y. |
author_sort | McKay, Isabelle R. |
collection | PubMed |
description | Cystic fibrosis (CF) is a common disorder of autosomal recessive inheritance, that once conferred a life expectancy of only a few months. Over recent years, significant advances have been made to CF therapeutic approaches, changing the face of the disease, and facilitating the partial restoration of pancreatic function. This mini review summarizes the current landscape of exocrine pancreatic management in CF and explores areas for future direction and development. |
format | Online Article Text |
id | pubmed-9271761 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2022 |
publisher | Frontiers Media S.A. |
record_format | MEDLINE/PubMed |
spelling | pubmed-92717612022-07-12 The Exocrine Pancreas in Cystic Fibrosis in the Era of CFTR Modulation: A Mini Review McKay, Isabelle R. Ooi, Chee Y. Front Pediatr Pediatrics Cystic fibrosis (CF) is a common disorder of autosomal recessive inheritance, that once conferred a life expectancy of only a few months. Over recent years, significant advances have been made to CF therapeutic approaches, changing the face of the disease, and facilitating the partial restoration of pancreatic function. This mini review summarizes the current landscape of exocrine pancreatic management in CF and explores areas for future direction and development. Frontiers Media S.A. 2022-06-27 /pmc/articles/PMC9271761/ /pubmed/35832587 http://dx.doi.org/10.3389/fped.2022.914790 Text en Copyright © 2022 McKay and Ooi. https://creativecommons.org/licenses/by/4.0/This is an open-access article distributed under the terms of the Creative Commons Attribution License (CC BY). The use, distribution or reproduction in other forums is permitted, provided the original author(s) and the copyright owner(s) are credited and that the original publication in this journal is cited, in accordance with accepted academic practice. No use, distribution or reproduction is permitted which does not comply with these terms. |
spellingShingle | Pediatrics McKay, Isabelle R. Ooi, Chee Y. The Exocrine Pancreas in Cystic Fibrosis in the Era of CFTR Modulation: A Mini Review |
title | The Exocrine Pancreas in Cystic Fibrosis in the Era of CFTR Modulation: A Mini Review |
title_full | The Exocrine Pancreas in Cystic Fibrosis in the Era of CFTR Modulation: A Mini Review |
title_fullStr | The Exocrine Pancreas in Cystic Fibrosis in the Era of CFTR Modulation: A Mini Review |
title_full_unstemmed | The Exocrine Pancreas in Cystic Fibrosis in the Era of CFTR Modulation: A Mini Review |
title_short | The Exocrine Pancreas in Cystic Fibrosis in the Era of CFTR Modulation: A Mini Review |
title_sort | exocrine pancreas in cystic fibrosis in the era of cftr modulation: a mini review |
topic | Pediatrics |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9271761/ https://www.ncbi.nlm.nih.gov/pubmed/35832587 http://dx.doi.org/10.3389/fped.2022.914790 |
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