The Exocrine Pancreas in Cystic Fibrosis in the Era of CFTR Modulation: A Mini Review

Cystic fibrosis (CF) is a common disorder of autosomal recessive inheritance, that once conferred a life expectancy of only a few months. Over recent years, significant advances have been made to CF therapeutic approaches, changing the face of the disease, and facilitating the partial restoration of...

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Autores principales: McKay, Isabelle R., Ooi, Chee Y.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9271761/
https://www.ncbi.nlm.nih.gov/pubmed/35832587
http://dx.doi.org/10.3389/fped.2022.914790
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author McKay, Isabelle R.
Ooi, Chee Y.
author_facet McKay, Isabelle R.
Ooi, Chee Y.
author_sort McKay, Isabelle R.
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description Cystic fibrosis (CF) is a common disorder of autosomal recessive inheritance, that once conferred a life expectancy of only a few months. Over recent years, significant advances have been made to CF therapeutic approaches, changing the face of the disease, and facilitating the partial restoration of pancreatic function. This mini review summarizes the current landscape of exocrine pancreatic management in CF and explores areas for future direction and development.
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spelling pubmed-92717612022-07-12 The Exocrine Pancreas in Cystic Fibrosis in the Era of CFTR Modulation: A Mini Review McKay, Isabelle R. Ooi, Chee Y. Front Pediatr Pediatrics Cystic fibrosis (CF) is a common disorder of autosomal recessive inheritance, that once conferred a life expectancy of only a few months. Over recent years, significant advances have been made to CF therapeutic approaches, changing the face of the disease, and facilitating the partial restoration of pancreatic function. This mini review summarizes the current landscape of exocrine pancreatic management in CF and explores areas for future direction and development. Frontiers Media S.A. 2022-06-27 /pmc/articles/PMC9271761/ /pubmed/35832587 http://dx.doi.org/10.3389/fped.2022.914790 Text en Copyright © 2022 McKay and Ooi. https://creativecommons.org/licenses/by/4.0/This is an open-access article distributed under the terms of the Creative Commons Attribution License (CC BY). The use, distribution or reproduction in other forums is permitted, provided the original author(s) and the copyright owner(s) are credited and that the original publication in this journal is cited, in accordance with accepted academic practice. No use, distribution or reproduction is permitted which does not comply with these terms.
spellingShingle Pediatrics
McKay, Isabelle R.
Ooi, Chee Y.
The Exocrine Pancreas in Cystic Fibrosis in the Era of CFTR Modulation: A Mini Review
title The Exocrine Pancreas in Cystic Fibrosis in the Era of CFTR Modulation: A Mini Review
title_full The Exocrine Pancreas in Cystic Fibrosis in the Era of CFTR Modulation: A Mini Review
title_fullStr The Exocrine Pancreas in Cystic Fibrosis in the Era of CFTR Modulation: A Mini Review
title_full_unstemmed The Exocrine Pancreas in Cystic Fibrosis in the Era of CFTR Modulation: A Mini Review
title_short The Exocrine Pancreas in Cystic Fibrosis in the Era of CFTR Modulation: A Mini Review
title_sort exocrine pancreas in cystic fibrosis in the era of cftr modulation: a mini review
topic Pediatrics
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9271761/
https://www.ncbi.nlm.nih.gov/pubmed/35832587
http://dx.doi.org/10.3389/fped.2022.914790
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