Cargando…

Raynaud’s Phenomenon and Limb Hypertrophy Presenting Phacomatosis Pigmentovascularis: A Rare Association

Phacomatosis pigmentovascularis is a rare dermal disorder attributed to the presence of various nevi. These lesions exist since birth, so the patient remains well aware of them. Various systemic involvements may be associated with the nevus, but the association of Raynaud’s phenomenon is seldom repo...

Descripción completa

Detalles Bibliográficos
Autores principales: Pipal, Dharmendra K, Pipal, Rajendra K, Verma, Vijay, Pipal, Vibha Rani, Yadav, Seema
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9278798/
https://www.ncbi.nlm.nih.gov/pubmed/35844310
http://dx.doi.org/10.7759/cureus.25900
Descripción
Sumario:Phacomatosis pigmentovascularis is a rare dermal disorder attributed to the presence of various nevi. These lesions exist since birth, so the patient remains well aware of them. Various systemic involvements may be associated with the nevus, but the association of Raynaud’s phenomenon is seldom reported. Our patient came with similar features and, on workup, no neurovascular compression was present, such as cervical rib or thoracic outlet syndrome. Therefore, he was managed conservatively and experienced improvement following the treatment. The objective of reporting this case is to highlight the association of Raynaud's phenomenon with such nervous lesions.