Pulmonary artery aneurysm: Harbinger of an ominous disease

An 11-year-old girl presented with chronic cough and recurrent hemoptysis. On examination, she had features of right heart failure and cyanosis, with severe pulmonary hypertension on echocardiogram. Computed tomography pulmonary angiography showed aneurysmal dilatations of the pulmonary artery with...

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Detalles Bibliográficos
Autores principales: Bhattacharya, Deepanjan, Sasikumar, Deepa, Anoop, Ayyappan, Valakada, Jineesh, Naik, Nitin, Dharan, Baiju Sasi
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer - Medknow 2022
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9280089/
https://www.ncbi.nlm.nih.gov/pubmed/35847388
http://dx.doi.org/10.4103/apc.apc_49_21
Descripción
Sumario:An 11-year-old girl presented with chronic cough and recurrent hemoptysis. On examination, she had features of right heart failure and cyanosis, with severe pulmonary hypertension on echocardiogram. Computed tomography pulmonary angiography showed aneurysmal dilatations of the pulmonary artery with elevated erythrocyte sedimentation rate and C-reactive protein and positive human leukocyte antigen B51. A diagnosis of Hughes–Stovin syndrome (vascular variant of Behcet's syndrome) was confirmed, and she was started on immunosuppression, on which there was improvement.

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