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Biliary atresia and congenital disorders of the extrahepatic bile ducts
Biliary atresia (BA) and choledochal cysts are diseases of the intrahepatic and extrahepatic biliary tree. While their exact etiopathogeneses are not known, they should be treated promptly due to the potential for irreversible parenchymal liver disease. A diagnosis of BA may be easy or complicated,...
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Baishideng Publishing Group Inc
2022
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Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9297290/ https://www.ncbi.nlm.nih.gov/pubmed/36051179 http://dx.doi.org/10.4292/wjgpt.v13.i4.33 |
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author | Islek, Ali Tumgor, Gokhan |
author_facet | Islek, Ali Tumgor, Gokhan |
author_sort | Islek, Ali |
collection | PubMed |
description | Biliary atresia (BA) and choledochal cysts are diseases of the intrahepatic and extrahepatic biliary tree. While their exact etiopathogeneses are not known, they should be treated promptly due to the potential for irreversible parenchymal liver disease. A diagnosis of BA may be easy or complicated, but should not be delayed. BA is always treated surgically, and performing the surgery before the age of 2 mo greatly increases its effectiveness and extends the time until the need for liver transplantation arises. While the more common types of choledochal cysts require surgical treatment, some can be treated with endoscopic retrograde cholangiopancreatography. Choledochal cysts may cause recurrent cholangitis and the potential for malignancy should not be ignored. |
format | Online Article Text |
id | pubmed-9297290 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2022 |
publisher | Baishideng Publishing Group Inc |
record_format | MEDLINE/PubMed |
spelling | pubmed-92972902022-08-31 Biliary atresia and congenital disorders of the extrahepatic bile ducts Islek, Ali Tumgor, Gokhan World J Gastrointest Pharmacol Ther Minireviews Biliary atresia (BA) and choledochal cysts are diseases of the intrahepatic and extrahepatic biliary tree. While their exact etiopathogeneses are not known, they should be treated promptly due to the potential for irreversible parenchymal liver disease. A diagnosis of BA may be easy or complicated, but should not be delayed. BA is always treated surgically, and performing the surgery before the age of 2 mo greatly increases its effectiveness and extends the time until the need for liver transplantation arises. While the more common types of choledochal cysts require surgical treatment, some can be treated with endoscopic retrograde cholangiopancreatography. Choledochal cysts may cause recurrent cholangitis and the potential for malignancy should not be ignored. Baishideng Publishing Group Inc 2022-07-05 2022-07-05 /pmc/articles/PMC9297290/ /pubmed/36051179 http://dx.doi.org/10.4292/wjgpt.v13.i4.33 Text en ©The Author(s) 2022. Published by Baishideng Publishing Group Inc. All rights reserved. https://creativecommons.org/licenses/by-nc/4.0/This article is an open-access article that was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Commons Attribution NonCommercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: https://creativecommons.org/Licenses/by-nc/4.0/ |
spellingShingle | Minireviews Islek, Ali Tumgor, Gokhan Biliary atresia and congenital disorders of the extrahepatic bile ducts |
title | Biliary atresia and congenital disorders of the extrahepatic bile ducts |
title_full | Biliary atresia and congenital disorders of the extrahepatic bile ducts |
title_fullStr | Biliary atresia and congenital disorders of the extrahepatic bile ducts |
title_full_unstemmed | Biliary atresia and congenital disorders of the extrahepatic bile ducts |
title_short | Biliary atresia and congenital disorders of the extrahepatic bile ducts |
title_sort | biliary atresia and congenital disorders of the extrahepatic bile ducts |
topic | Minireviews |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9297290/ https://www.ncbi.nlm.nih.gov/pubmed/36051179 http://dx.doi.org/10.4292/wjgpt.v13.i4.33 |
work_keys_str_mv | AT islekali biliaryatresiaandcongenitaldisordersoftheextrahepaticbileducts AT tumgorgokhan biliaryatresiaandcongenitaldisordersoftheextrahepaticbileducts |