Pediatric cystectomy for refractory cystitis post-bone marrow transplant in dyskeratosis congenita: A case report

We present a case of refractory cystitis after BK-virus associated hemorrhagic cystitis following bone marrow transplantation requiring cystectomy in a 17-year-old female with genetically confirmed dyskeratosis congenita, a telomere disorder characterized by early bone marrow failure. She presented...

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Detalles Bibliográficos
Autores principales: Robinson, Eric, Seideman, Casey, Wong, Trisha, Hakar, Melanie, Austin, J. Christopher
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2022
Materias:
Pediatrics
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9303813/
https://www.ncbi.nlm.nih.gov/pubmed/35873895
http://dx.doi.org/10.1016/j.eucr.2022.102163
Descripción
Sumario:We present a case of refractory cystitis after BK-virus associated hemorrhagic cystitis following bone marrow transplantation requiring cystectomy in a 17-year-old female with genetically confirmed dyskeratosis congenita, a telomere disorder characterized by early bone marrow failure. She presented with a contracted, small bladder with intense urinary symptoms non-responsive to conservative therapy and requiring opioids for pain control. Cystectomy is a rare, final surgical treatment for benign bladder conditions, especially among younger patients, and she experienced successful resolution of symptoms and cessation of chronic opioids post-intervention.

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