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Neurodegeneration and neuroinflammation are linked, but independent of alpha‐synuclein inclusions, in a seeding/spreading mouse model of Parkinson's disease

A key pathological process in Parkinson's disease (PD) is the transneuronal spreading of α‐synuclein. Alpha‐synuclein (α‐syn) is a presynaptic protein that, in PD, forms pathological inclusions. Other hallmarks of PD include neurodegeneration and microgliosis in susceptible brain regions. Wheth...

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Autores principales: Garcia, Pierre, Jürgens‐Wemheuer, Wiebke, Uriarte Huarte, Oihane, Michelucci, Alessandro, Masuch, Annette, Brioschi, Simone, Weihofen, Andreas, Koncina, Eric, Coowar, Djalil, Heurtaux, Tony, Glaab, Enrico, Balling, Rudi, Sousa, Carole, Kaoma, Tony, Nicot, Nathalie, Pfander, Tatjana, Schulz‐Schaeffer, Walter, Allouche, Ahmad, Fischer, Nicolas, Biber, Knut, Kleine‐Borgmann, Felix, Mittelbronn, Michel, Ostaszewski, Marek, Schmit, Kristopher J., Buttini, Manuel
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley & Sons, Inc. 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9305192/
https://www.ncbi.nlm.nih.gov/pubmed/35092321
http://dx.doi.org/10.1002/glia.24149
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author Garcia, Pierre
Jürgens‐Wemheuer, Wiebke
Uriarte Huarte, Oihane
Michelucci, Alessandro
Masuch, Annette
Brioschi, Simone
Weihofen, Andreas
Koncina, Eric
Coowar, Djalil
Heurtaux, Tony
Glaab, Enrico
Balling, Rudi
Sousa, Carole
Kaoma, Tony
Nicot, Nathalie
Pfander, Tatjana
Schulz‐Schaeffer, Walter
Allouche, Ahmad
Fischer, Nicolas
Biber, Knut
Kleine‐Borgmann, Felix
Mittelbronn, Michel
Ostaszewski, Marek
Schmit, Kristopher J.
Buttini, Manuel
author_facet Garcia, Pierre
Jürgens‐Wemheuer, Wiebke
Uriarte Huarte, Oihane
Michelucci, Alessandro
Masuch, Annette
Brioschi, Simone
Weihofen, Andreas
Koncina, Eric
Coowar, Djalil
Heurtaux, Tony
Glaab, Enrico
Balling, Rudi
Sousa, Carole
Kaoma, Tony
Nicot, Nathalie
Pfander, Tatjana
Schulz‐Schaeffer, Walter
Allouche, Ahmad
Fischer, Nicolas
Biber, Knut
Kleine‐Borgmann, Felix
Mittelbronn, Michel
Ostaszewski, Marek
Schmit, Kristopher J.
Buttini, Manuel
author_sort Garcia, Pierre
collection PubMed
description A key pathological process in Parkinson's disease (PD) is the transneuronal spreading of α‐synuclein. Alpha‐synuclein (α‐syn) is a presynaptic protein that, in PD, forms pathological inclusions. Other hallmarks of PD include neurodegeneration and microgliosis in susceptible brain regions. Whether it is primarily transneuronal spreading of α‐syn particles, inclusion formation, or other mechanisms, such as inflammation, that cause neurodegeneration in PD is unclear. We used a model of spreading of α‐syn induced by striatal injection of α‐syn preformed fibrils into the mouse striatum to address this question. We performed quantitative analysis for α‐syn inclusions, neurodegeneration, and microgliosis in different brain regions, and generated gene expression profiles of the ventral midbrain, at two different timepoints after disease induction. We observed significant neurodegeneration and microgliosis in brain regions not only with, but also without α‐syn inclusions. We also observed prominent microgliosis in injured brain regions that did not correlate with neurodegeneration nor with inclusion load. Using longitudinal gene expression profiling, we observed early gene expression changes, linked to neuroinflammation, that preceded neurodegeneration, indicating an active role of microglia in this process. Altered gene pathways overlapped with those typical of PD. Our observations indicate that α‐syn inclusion formation is not the major driver in the early phases of PD‐like neurodegeneration, but that microglia, activated by diffusible, oligomeric α‐syn, may play a key role in this process. Our findings uncover new features of α‐syn induced pathologies, in particular microgliosis, and point to the necessity for a broader view of the process of α‐syn spreading.
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spelling pubmed-93051922022-07-28 Neurodegeneration and neuroinflammation are linked, but independent of alpha‐synuclein inclusions, in a seeding/spreading mouse model of Parkinson's disease Garcia, Pierre Jürgens‐Wemheuer, Wiebke Uriarte Huarte, Oihane Michelucci, Alessandro Masuch, Annette Brioschi, Simone Weihofen, Andreas Koncina, Eric Coowar, Djalil Heurtaux, Tony Glaab, Enrico Balling, Rudi Sousa, Carole Kaoma, Tony Nicot, Nathalie Pfander, Tatjana Schulz‐Schaeffer, Walter Allouche, Ahmad Fischer, Nicolas Biber, Knut Kleine‐Borgmann, Felix Mittelbronn, Michel Ostaszewski, Marek Schmit, Kristopher J. Buttini, Manuel Glia Research Articles A key pathological process in Parkinson's disease (PD) is the transneuronal spreading of α‐synuclein. Alpha‐synuclein (α‐syn) is a presynaptic protein that, in PD, forms pathological inclusions. Other hallmarks of PD include neurodegeneration and microgliosis in susceptible brain regions. Whether it is primarily transneuronal spreading of α‐syn particles, inclusion formation, or other mechanisms, such as inflammation, that cause neurodegeneration in PD is unclear. We used a model of spreading of α‐syn induced by striatal injection of α‐syn preformed fibrils into the mouse striatum to address this question. We performed quantitative analysis for α‐syn inclusions, neurodegeneration, and microgliosis in different brain regions, and generated gene expression profiles of the ventral midbrain, at two different timepoints after disease induction. We observed significant neurodegeneration and microgliosis in brain regions not only with, but also without α‐syn inclusions. We also observed prominent microgliosis in injured brain regions that did not correlate with neurodegeneration nor with inclusion load. Using longitudinal gene expression profiling, we observed early gene expression changes, linked to neuroinflammation, that preceded neurodegeneration, indicating an active role of microglia in this process. Altered gene pathways overlapped with those typical of PD. Our observations indicate that α‐syn inclusion formation is not the major driver in the early phases of PD‐like neurodegeneration, but that microglia, activated by diffusible, oligomeric α‐syn, may play a key role in this process. Our findings uncover new features of α‐syn induced pathologies, in particular microgliosis, and point to the necessity for a broader view of the process of α‐syn spreading. John Wiley & Sons, Inc. 2022-01-29 2022-05 /pmc/articles/PMC9305192/ /pubmed/35092321 http://dx.doi.org/10.1002/glia.24149 Text en © 2022 The Authors. GLIA published by Wiley Periodicals LLC. https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open access article under the terms of the http://creativecommons.org/licenses/by-nc-nd/4.0/ (https://creativecommons.org/licenses/by-nc-nd/4.0/) License, which permits use and distribution in any medium, provided the original work is properly cited, the use is non‐commercial and no modifications or adaptations are made.
spellingShingle Research Articles
Garcia, Pierre
Jürgens‐Wemheuer, Wiebke
Uriarte Huarte, Oihane
Michelucci, Alessandro
Masuch, Annette
Brioschi, Simone
Weihofen, Andreas
Koncina, Eric
Coowar, Djalil
Heurtaux, Tony
Glaab, Enrico
Balling, Rudi
Sousa, Carole
Kaoma, Tony
Nicot, Nathalie
Pfander, Tatjana
Schulz‐Schaeffer, Walter
Allouche, Ahmad
Fischer, Nicolas
Biber, Knut
Kleine‐Borgmann, Felix
Mittelbronn, Michel
Ostaszewski, Marek
Schmit, Kristopher J.
Buttini, Manuel
Neurodegeneration and neuroinflammation are linked, but independent of alpha‐synuclein inclusions, in a seeding/spreading mouse model of Parkinson's disease
title Neurodegeneration and neuroinflammation are linked, but independent of alpha‐synuclein inclusions, in a seeding/spreading mouse model of Parkinson's disease
title_full Neurodegeneration and neuroinflammation are linked, but independent of alpha‐synuclein inclusions, in a seeding/spreading mouse model of Parkinson's disease
title_fullStr Neurodegeneration and neuroinflammation are linked, but independent of alpha‐synuclein inclusions, in a seeding/spreading mouse model of Parkinson's disease
title_full_unstemmed Neurodegeneration and neuroinflammation are linked, but independent of alpha‐synuclein inclusions, in a seeding/spreading mouse model of Parkinson's disease
title_short Neurodegeneration and neuroinflammation are linked, but independent of alpha‐synuclein inclusions, in a seeding/spreading mouse model of Parkinson's disease
title_sort neurodegeneration and neuroinflammation are linked, but independent of alpha‐synuclein inclusions, in a seeding/spreading mouse model of parkinson's disease
topic Research Articles
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9305192/
https://www.ncbi.nlm.nih.gov/pubmed/35092321
http://dx.doi.org/10.1002/glia.24149
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