Lymphangiography as a Treatment for Refractory Congenital Chylothorax Due to RASopathies: A Report of Two Cases

In this study, we report two cases in which intranodal lymphangiography helped improve congenital chylothorax due to RASopathies. We performed lymphangiography after conservative treatments failed to improve chylothorax in an 8-year-old girl with cardiofaciocutaneous syndrome and a 2-month-old boy w...

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Detalles Bibliográficos
Autores principales: Kinota, Naoya, Kodama, Hiroshi, Moriyama, Taiki, Taniguchi, Junichi, Maruyama, Mitsunari, Ogasawara, Atsushi, Kako, Yasukazu, Kobayashi, Kaoru, Takaki, Haruyuki, Shibata, Akio, Minagawa, Kyoko, Takeshima, Yasuhiro, Yamakado, Koichiro
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The Japanese Society of Interventional Radiology 2022
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9327383/
https://www.ncbi.nlm.nih.gov/pubmed/35911871
http://dx.doi.org/10.22575/interventionalradiology.2021-0014
Descripción
Sumario:In this study, we report two cases in which intranodal lymphangiography helped improve congenital chylothorax due to RASopathies. We performed lymphangiography after conservative treatments failed to improve chylothorax in an 8-year-old girl with cardiofaciocutaneous syndrome and a 2-month-old boy with Noonan syndrome. Inguinal lymph nodes were punctured with 25-gauge needles under ultrasonographic guidance, and 4 and 1 mL of iodized oil were injected, respectively, showing a backflow of iodized oil into the lungs. Chylothorax had improved in both patients after nodal lymphangiography. However, the second child experienced worsening of disease-associated extremity edema and died of sepsis 4 months later.

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