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Wolf in sheep's clothing: Primary orbital Ewing sarcoma in a child masquerading as internal angular dermoid

Ewing sarcoma is one of the rare, highly malignant neuroectodermal tumors frequently involving bones. Primary orbital Ewing sarcoma is extremely uncommon. We report a rare case of a 5-year-old boy who presented to us with a painless, slow-growing mass above the medial canthus of the left eye, the cl...

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Detalles Bibliográficos
Autores principales: Mendonca, Teena Mariet, Lashkari, Harsha Prasada, Suresh, Pooja K, Kondaveti, Rahul, Ali, Faraz, Rodrigues, Gladys R
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer - Medknow 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9351945/
https://www.ncbi.nlm.nih.gov/pubmed/35937728
http://dx.doi.org/10.4103/ojo.ojo_180_21
Descripción
Sumario:Ewing sarcoma is one of the rare, highly malignant neuroectodermal tumors frequently involving bones. Primary orbital Ewing sarcoma is extremely uncommon. We report a rare case of a 5-year-old boy who presented to us with a painless, slow-growing mass above the medial canthus of the left eye, the clinical appearance of which was masquerading as an internal angular dermoid. The child was subsequently diagnosed to have primary orbital Ewing sarcoma. Primary orbital Ewing sarcoma is a rare tumor with poor prognosis, poses diagnostic challenges, and demands a high index of clinical suspicion.