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Abdominal aortic aneurysm in a child with tuberous sclerosis
Abdominal aortic aneurysm is rare in the pediatric population and even more uncommon in association with tuberous sclerosis. We have presented a unique case of a 3-year, 8-month-old girl who was successfully treated. She was admitted because of breakthrough seizures. A painless pulsatile abdominal m...
Autores principales: | , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Elsevier
2022
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9352511/ https://www.ncbi.nlm.nih.gov/pubmed/35936020 http://dx.doi.org/10.1016/j.jvscit.2022.05.018 |
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author | Gruhl, Sabrina Lasini Tham, Yi Chuan Lee, York Tien Nakao, Masakazu |
author_facet | Gruhl, Sabrina Lasini Tham, Yi Chuan Lee, York Tien Nakao, Masakazu |
author_sort | Gruhl, Sabrina Lasini |
collection | PubMed |
description | Abdominal aortic aneurysm is rare in the pediatric population and even more uncommon in association with tuberous sclerosis. We have presented a unique case of a 3-year, 8-month-old girl who was successfully treated. She was admitted because of breakthrough seizures. A painless pulsatile abdominal mass on examination prompted an abdominal ultrasound scan, which identified a large saccular abdominal aortic aneurysm. Urgent replacement of the abdominal aorta with a 12-mm woven Dacron graft was undertaken. A postoperative ultrasound evaluation confirmed the successful repair. She was growing well when examined 7 months after surgery. |
format | Online Article Text |
id | pubmed-9352511 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2022 |
publisher | Elsevier |
record_format | MEDLINE/PubMed |
spelling | pubmed-93525112022-08-05 Abdominal aortic aneurysm in a child with tuberous sclerosis Gruhl, Sabrina Lasini Tham, Yi Chuan Lee, York Tien Nakao, Masakazu J Vasc Surg Cases Innov Tech Case report Abdominal aortic aneurysm is rare in the pediatric population and even more uncommon in association with tuberous sclerosis. We have presented a unique case of a 3-year, 8-month-old girl who was successfully treated. She was admitted because of breakthrough seizures. A painless pulsatile abdominal mass on examination prompted an abdominal ultrasound scan, which identified a large saccular abdominal aortic aneurysm. Urgent replacement of the abdominal aorta with a 12-mm woven Dacron graft was undertaken. A postoperative ultrasound evaluation confirmed the successful repair. She was growing well when examined 7 months after surgery. Elsevier 2022-07-06 /pmc/articles/PMC9352511/ /pubmed/35936020 http://dx.doi.org/10.1016/j.jvscit.2022.05.018 Text en © 2022 The Author(s) https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/). |
spellingShingle | Case report Gruhl, Sabrina Lasini Tham, Yi Chuan Lee, York Tien Nakao, Masakazu Abdominal aortic aneurysm in a child with tuberous sclerosis |
title | Abdominal aortic aneurysm in a child with tuberous sclerosis |
title_full | Abdominal aortic aneurysm in a child with tuberous sclerosis |
title_fullStr | Abdominal aortic aneurysm in a child with tuberous sclerosis |
title_full_unstemmed | Abdominal aortic aneurysm in a child with tuberous sclerosis |
title_short | Abdominal aortic aneurysm in a child with tuberous sclerosis |
title_sort | abdominal aortic aneurysm in a child with tuberous sclerosis |
topic | Case report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9352511/ https://www.ncbi.nlm.nih.gov/pubmed/35936020 http://dx.doi.org/10.1016/j.jvscit.2022.05.018 |
work_keys_str_mv | AT gruhlsabrinalasini abdominalaorticaneurysminachildwithtuberoussclerosis AT thamyichuan abdominalaorticaneurysminachildwithtuberoussclerosis AT leeyorktien abdominalaorticaneurysminachildwithtuberoussclerosis AT nakaomasakazu abdominalaorticaneurysminachildwithtuberoussclerosis |